Ruptured ulnar artery aneurysm in vascular Ehlers-Danlos syndrome.
Connective tissue disorder
Ehlers Danlos Syndrome
Peripheral aneurysm
Journal
Journal of vascular surgery cases and innovative techniques
ISSN: 2468-4287
Titre abrégé: J Vasc Surg Cases Innov Tech
Pays: United States
ID NLM: 101701125
Informations de publication
Date de publication:
Mar 2020
Mar 2020
Historique:
received:
30
09
2019
accepted:
21
11
2019
entrez:
20
2
2020
pubmed:
20
2
2020
medline:
20
2
2020
Statut:
epublish
Résumé
Vascular Ehlers-Danlos syndrome (vEDS), also known as type IV Ehlers-Danlos syndrome, is a rare inherited connective tissue disease that affects 1 in 50,000 to 250,000 individuals. It is characterized by catastrophic vascular complications and hollow viscus rupture; 80% of patients with vEDS experience a vascular complication by the age of 40 years, and median life expectancy is 40 to 50 years. The central vasculature and visceral vasculature are most commonly affected; peripheral involvement is much less common. We describe the case of a 40-year-old woman with vEDS previously complicated by ruptured splenic and posterior tibial artery aneurysms who presented with a ruptured left ulnar artery aneurysm resulting in compartment syndrome.
Identifiants
pubmed: 32072093
doi: 10.1016/j.jvscit.2019.11.013
pii: S2468-4287(19)30152-2
pmc: PMC7016348
doi:
Types de publication
Case Reports
Langues
eng
Pagination
71-74Informations de copyright
© 2019 The Author(s).
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