Chromosome Transplantation: A Possible Approach to Treat Human X-linked Disorders.

chromosome transfer chromosome transplantation genetic therapy genomic disorders induced pluripotent stem cells

Journal

Molecular therapy. Methods & clinical development
ISSN: 2329-0501
Titre abrégé: Mol Ther Methods Clin Dev
Pays: United States
ID NLM: 101624857

Informations de publication

Date de publication:
12 Jun 2020
Historique:
received: 21 10 2019
accepted: 07 01 2020
entrez: 27 2 2020
pubmed: 27 2 2020
medline: 27 2 2020
Statut: epublish

Résumé

Many human genetic diseases are associated with gross mutations such as aneuploidies, deletions, duplications, or inversions. For these "structural" disorders, conventional gene therapy, based on viral vectors and/or on programmable nuclease-mediated homologous recombination, is still unsatisfactory. To correct such disorders, chromosome transplantation (CT), defined as the perfect substitution of an endogenous defective chromosome with an exogenous normal one, could be applied. CT re-establishes a normal diploid cell, leaving no marker of the procedure, as we have recently shown in mouse pluripotent stem cells. To prove the feasibility of the CT approach in human cells, we used human induced pluripotent stem cells (hiPSCs) reprogrammed from Lesch-Nyhan (LN) disease patients, taking advantage of their mutation in the X-linked

Identifiants

pubmed: 32099849
doi: 10.1016/j.omtm.2020.01.003
pii: S2329-0501(20)30014-0
pmc: PMC7029378
doi:

Types de publication

Journal Article

Langues

eng

Pagination

369-377

Informations de copyright

© 2020 The Author(s).

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Auteurs

Marianna Paulis (M)

National Research Council (CNR)-IRGB/UOS, Milan, Italy.
Humanitas Clinical and Research Center, Rozzano (MI), Italy.

Lucia Susani (L)

National Research Council (CNR)-IRGB/UOS, Milan, Italy.
Humanitas Clinical and Research Center, Rozzano (MI), Italy.

Alessandra Castelli (A)

National Research Council (CNR)-IRGB/UOS, Milan, Italy.
Humanitas Clinical and Research Center, Rozzano (MI), Italy.

Teruhiko Suzuki (T)

Stem Cell Project, Tokyo Metropolitan Institute of Medical Science, Tokyo, Japan.

Takahiko Hara (T)

Stem Cell Project, Tokyo Metropolitan Institute of Medical Science, Tokyo, Japan.

Letizia Straniero (L)

Department of Biomedical Sciences, Humanitas University, Pieve Emanuele (MI), Italy.

Stefano Duga (S)

Humanitas Clinical and Research Center, Rozzano (MI), Italy.
Department of Biomedical Sciences, Humanitas University, Pieve Emanuele (MI), Italy.

Dario Strina (D)

National Research Council (CNR)-IRGB/UOS, Milan, Italy.
Humanitas Clinical and Research Center, Rozzano (MI), Italy.

Stefano Mantero (S)

National Research Council (CNR)-IRGB/UOS, Milan, Italy.
Humanitas Clinical and Research Center, Rozzano (MI), Italy.

Elena Caldana (E)

National Research Council (CNR)-IRGB/UOS, Milan, Italy.
Humanitas Clinical and Research Center, Rozzano (MI), Italy.

Lucia Sergi Sergi (LS)

San Raffaele-TIGET, Milan, Italy.

Anna Villa (A)

National Research Council (CNR)-IRGB/UOS, Milan, Italy.
San Raffaele-TIGET, Milan, Italy.

Paolo Vezzoni (P)

National Research Council (CNR)-IRGB/UOS, Milan, Italy.
Humanitas Clinical and Research Center, Rozzano (MI), Italy.

Classifications MeSH