Pulmonary Arterial Hypertension in Connective Tissue Disorders: The emerging role of screening and early diagnosis. A position paper for Greek Rheumatologists.

Pulmonary arterial hypertension connective tissue disorders scleroderma

Journal

Mediterranean journal of rheumatology
ISSN: 2529-198X
Titre abrégé: Mediterr J Rheumatol
Pays: Greece
ID NLM: 101730166

Informations de publication

Date de publication:
Jun 2019
Historique:
received: 29 04 2019
revised: 19 06 2019
accepted: 28 06 2019
entrez: 19 3 2020
pubmed: 19 3 2020
medline: 19 3 2020
Statut: epublish

Résumé

Pulmonary Arterial Hypertension is regarded as a devastating disease, complicating Connective Tissue Diseases. Although much progress has been achieved in the last 20 years, several unfulfilled needs in diagnosis and management of PAH in these patients may still be identified. After a systematic review of the literature and integrating results from the latest research articles, key clinical issues for the screening and diagnosis of Pulmonary Arterial Hypertension in Connective Tissue Disorder Patients and specifically Scleroderma patients are described in this article, allowing physicians to contribute to early diagnosis of patients with Scleroderma-associated Pulmonary Arterial Hypertension.

Identifiants

pubmed: 32185347
doi: 10.31138/mjr.30.2.90
pii: mjr-30-2-90
pmc: PMC7045968
doi:

Types de publication

Journal Article Review

Langues

eng

Pagination

90-93

Informations de copyright

© 2019 The Mediterranean Journal of Rheumatology (MJR).

Références

Eur Respir J. 2019 Jan 24;53(1):
pubmed: 30545968
Arthritis Rheum. 2013 Sep;65(9):2412-23
pubmed: 23740572
Arthritis Care Res (Hoboken). 2014 Sep;66(9):1386-94
pubmed: 24515598
Eur Respir J. 2019 Jan 24;53(1):
pubmed: 30545972
Eur Respir J. 2015 Oct;46(4):903-75
pubmed: 26318161
Eur Respir J. 2018 Apr 4;51(4):
pubmed: 29563168
Ann Rheum Dis. 2014 Jul;73(7):1340-9
pubmed: 23687283
Chest. 2018 Oct;154(4):862-871
pubmed: 29777655
Ann Rheum Dis. 2007 Jul;66(7):940-4
pubmed: 17329309
Curr Rheumatol Rep. 2016 Feb;18(2):10
pubmed: 26841964
Arthritis Rheum. 2006 Sep;54(9):3043-50
pubmed: 16947776
Arthritis Rheum. 2013 Apr;65(4):1074-84
pubmed: 23280155

Auteurs

Eftychia Demerouti (E)

Onassis Cardiac Surgery Center, Pulmonary Hypertension Unit, Athens, Greece.

Iraklis Tsangaris (I)

Attikon University Hospital, Pulmonary Hypertension Clinic, Athens, Greece.

Theodoros Dimitroulas (T)

4th Department of Internal Medicine, Hippokration Hospital, Thessaloniki, Greece.

George Giannakoulas (G)

AHEPA University General Hospital, Pulmonary Hypertension Unit, Thessaloniki, Greece.

Pelagia Katsimpri (P)

Rheumatology and Clinical Immunology Unit, "Attikon" University Hospital, Athens, Greece.

Ioanna Mitrouska (I)

Department of Thoracic Medicine, Faculty of Medicine, University of Crete, Crete, Greece.

Stylianos Orfanos (S)

Attikon University Hospital, Pulmonary Hypertension Clinic, Athens, Greece.

Ioannis Skoularigkis (I)

Department of Cardiology, Larissa University Hospital, Larissa, Greece.

Paraskevi Voulgari (P)

Rheumatology Clinic, Department of Internal Medicine, Medical School, University of Ioannina, Ioannina, Greece.

Petros Sfikakis (P)

First Department of Propaedeutic Internal Medicine and Rheumatology Unit, Medical School, National and Kapodistrian University of Athens, Athens, Greece.

Classifications MeSH