Primary adrenal leiomyosarcoma: A case report.

adrenal gland adrenalectomy leiomyosarcoma malignant neoplasia

Journal

Molecular and clinical oncology
ISSN: 2049-9450
Titre abrégé: Mol Clin Oncol
Pays: England
ID NLM: 101613422

Informations de publication

Date de publication:
Apr 2020
Historique:
received: 27 05 2019
accepted: 30 12 2019
entrez: 20 3 2020
pubmed: 20 3 2020
medline: 20 3 2020
Statut: ppublish

Résumé

Adrenal leiomyosarcomas are rare mesenchymal tumors of the suprarenal region that are usually diagnosed after they have reached a large size. We report the case of a 62-year-old male with an incidentally found left adrenal mass. Magnetic resonance imaging of the retroperitoneal space showed a heterogeneously enhanced mass, measuring 10x8.2 cm, with characteristics suspicious of malignancy. The patient underwent left radical adrenalectomy after the hormonal evaluation of the tumor due to the high probability of adrenocortical carcinoma. However, microscopic examination of the tumor showed a spindle cell sarcoma. Immunohistochemically the neoplastic cells were found positive for desmin and smooth muscle actin and the diagnosis of a well differentiated adrenal leiomyosarcoma was established. During follow-up the patient presented an aggressive course as he developed bone, liver and pulmonary metastases early postoperatively, which were treated with radiation therapy and chemotherapy. The patient has progressive metastatic disease while on chemotherapy 31 months after surgery.

Identifiants

pubmed: 32190312
doi: 10.3892/mco.2020.1987
pii: MCO-0-0-1987
pmc: PMC7057942
doi:

Types de publication

Journal Article

Langues

eng

Pagination

317-320

Informations de copyright

Copyright © 2019, Spandidos Publications.

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Auteurs

Maria Sakellariou (M)

Second Department of Surgery, School of Medicine, National and Kapodistrian University of Athens, Aretaieion University Hospital, 11528 Athens, Greece.

Dionysios Dellaportas (D)

Second Department of Surgery, School of Medicine, National and Kapodistrian University of Athens, Aretaieion University Hospital, 11528 Athens, Greece.

Eirini Grapsa (E)

Department of Nephrology, School of Medicine, National and Kapodistrian University of Athens, Aretaieion University Hospital, 11528 Athens, Greece.

Menelaos Tzikanoulas (M)

Department of Biopathology, School of Medicine, National and Kapodistrian University of Athens, Aretaieion University Hospital, 11528 Athens, Greece.

Athanasios Dellis (A)

Second Department of Surgery, School of Medicine, National and Kapodistrian University of Athens, Aretaieion University Hospital, 11528 Athens, Greece.

Theodosios Theodosopoulos (T)

Second Department of Surgery, School of Medicine, National and Kapodistrian University of Athens, Aretaieion University Hospital, 11528 Athens, Greece.

Constantinos Nastos (C)

Second Department of Surgery, School of Medicine, National and Kapodistrian University of Athens, Aretaieion University Hospital, 11528 Athens, Greece.

Classifications MeSH