G-CSF (filgrastim) treatment for amyotrophic lateral sclerosis: protocol for a phase II randomised, double-blind, placebo-controlled, parallel group, multicentre clinical study (STEMALS-II trial).


Journal

BMJ open
ISSN: 2044-6055
Titre abrégé: BMJ Open
Pays: England
ID NLM: 101552874

Informations de publication

Date de publication:
24 03 2020
Historique:
entrez: 27 3 2020
pubmed: 27 3 2020
medline: 14 4 2021
Statut: epublish

Résumé

Amyotrophic lateral sclerosis (ALS) is a fatal progressive neurological disorder characterised by a selective degeneration of motor neurons (MNs). Stem cell transplantation is considered as a promising strategy in neurological disorders therapy and the possibility of inducing bone marrow cells (BMCs) to circulate in the peripheral blood is suggested to investigate stem cells migration in degenerated ALS nerve tissues where potentially repair MN damage. Granulocyte-colony stimulating factor (G-CSF) is a growth factor which stimulates haematopoietic progenitor cells, mobilises BMCs into injured brain and it is itself a neurotrophic factor for MN. G-CSF safety in humans has been demonstrated and many observations suggest that it may affect neural cells. Therefore, we decided to use G-CSF to mobilise BMCs into the peripheral circulation in patients with ALS, planning a clinical trial to evaluate the effect of G-CSF administration in ALS patients compared with placebo. STEMALS-II is a phase II multicentre, randomised double-blind, placebo-controlled, parallel group clinical trial on G-CSF (filgrastim) and mannitol in ALS patients. Specifically, we investigate safety, tolerability and efficacy of four repeated courses of intravenous G-CSF and mannitol administered in 76 ALS patients in comparison with placebo (indistinguishable glucose solution 5%). We determine increase of G-CSF levels in serum and cerebrospinal fluid as CD34 The study protocol was approved by the Ethics Committee of Azienda Ospedaliera Universitaria 'Città della Salute e della Scienza', Torino, Italy. Results will be presented during scientific symposia or published in scientific journals. Eudract 2014-002228-28.

Identifiants

pubmed: 32209625
pii: bmjopen-2019-034049
doi: 10.1136/bmjopen-2019-034049
pmc: PMC7202695
doi:

Substances chimiques

Filgrastim PVI5M0M1GW

Banques de données

EudraCT
['2014-002228-28']

Types de publication

Clinical Trial Protocol Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

e034049

Investigateurs

A Bombaci (A)
M Brunetti (M)
S Cammarosano (S)
A Canosa (A)
C Calvo (C)
M Daviddi (M)
G De Marco (G)
P Cugnasco (P)
M Grassano (M)
B Iazzolino (B)
A Ilardi (A)
C Lauritano (C)
A Lomartire (A)
U Manera (U)
L Solero (L)
M C Torrieri R Vasta (MC)
M Gilestro (M)
V E Muccio P Omedé (VE)
F Gerardi (F)
C Cabona (C)
G Novi (G)
E Bersano (E)
F De Marchi (F)
R Spataro (R)
R Scimè (R)
A Fasano (A)
N Fini (N)
A Gessani (A)
E D'Errico (E)
A Scarafino (A)

Informations de copyright

© Author(s) (or their employer(s)) 2020. Re-use permitted under CC BY-NC. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

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Auteurs

Paolina Salamone (P)

'Rita Levi Montalcini' Department of Neuroscience, University of Turin, Torino, Piemonte, Italy.

Giuseppe Fuda (G)

'Rita Levi Montalcini' Department of Neuroscience, University of Turin, Torino, Piemonte, Italy.

Federico Casale (F)

'Rita Levi Montalcini' Department of Neuroscience, University of Turin, Torino, Piemonte, Italy federico.casale@unito.it.

Giuseppe Marrali (G)

'Rita Levi Montalcini' Department of Neuroscience, University of Turin, Torino, Piemonte, Italy.

Christian Lunetta (C)

NEuroMuscular Omnicentre (NEMO), Fondazione Serena Onlus, Milan, Italy.

Claudia Caponnetto (C)

Neurological Clinic, IRCCS Ospedale Policlinico San Martino, Genoa, Italy.

Letizia Mazzini (L)

Department of Neurology, Maggiore della Carità Hospital, University of Piemonte Orientale, Novara, Italy.

Vincenzo La Bella (V)

Department of Biomedicine, Neuroscience and Advanced Diagnostics, University of Palermo, Palermo, Sicilia, Italy.

Jessica Mandrioli (J)

Department of Neuroscience, Azienda Ospedaliera Universitaria Modena, St. Agostino-Estense Hospital, Modena, Italy.

Isabella Laura Simone (IL)

Neurology Unit, Department of Basic Medical Sciences, Neurosciences and Sense Organs, University of Bari, Bari, Puglia, Italy.

Cristina Moglia (C)

'Rita Levi Montalcini' Department of Neuroscience, University of Turin, Torino, Piemonte, Italy.
ALS Center, Azienda Ospedaliero Universitaria Città della Salute e della Scienza di Torino, Torino, Piemonte, Italy.

Andrea Calvo (A)

'Rita Levi Montalcini' Department of Neuroscience, University of Turin, Torino, Piemonte, Italy.
ALS Center, Azienda Ospedaliero Universitaria Città della Salute e della Scienza di Torino, Torino, Piemonte, Italy.

Corrado Tarella (C)

Oncohematology Division, IEO European Institute of Oncology, IRCCS, University of Milan, Milano, Lombardia, Italy.

Adriano Chio (A)

'Rita Levi Montalcini' Department of Neuroscience, University of Turin, Torino, Piemonte, Italy.
ALS Center, Azienda Ospedaliero Universitaria Città della Salute e della Scienza di Torino, Torino, Piemonte, Italy.

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