Acid Sphingomyelinase Downregulation Enhances Mitochondrial Fusion and Promotes Oxidative Metabolism in a Mouse Model of Melanoma.


Journal

Cells
ISSN: 2073-4409
Titre abrégé: Cells
Pays: Switzerland
ID NLM: 101600052

Informations de publication

Date de publication:
31 03 2020
Historique:
received: 13 02 2020
revised: 20 03 2020
accepted: 28 03 2020
entrez: 5 4 2020
pubmed: 5 4 2020
medline: 26 2 2021
Statut: epublish

Résumé

Melanoma is the most severe type of skin cancer. Its unique and heterogeneous metabolism, relying on both glycolysis and oxidative phosphorylation, allows it to adapt to disparate conditions. Mitochondrial function is strictly interconnected with mitochondrial dynamics and both are fundamental in tumour progression and metastasis. The malignant phenotype of melanoma is also regulated by the expression levels of the enzyme acid sphingomyelinase (A-SMase). By modulating at transcriptional level A-SMase in the melanoma cell line B16-F1 cells, we assessed the effect of enzyme downregulation on mitochondrial dynamics and function. Our results demonstrate that A-SMase influences mitochondrial morphology by affecting the expression of mitofusin 1 and OPA1. The enhanced expression of the two mitochondrial fusion proteins, observed when A-SMase is expressed at low levels, correlates with the increase of mitochondrial function via the stimulation of the genes PGC-1alpha and TFAM, two genes that preside over mitochondrial biogenesis. Thus, the reduction of A-SMase expression, observed in malignant melanomas, may determine their metastatic behaviour through the stimulation of mitochondrial fusion, activity and biogenesis, conferring a metabolic advantage to melanoma cells.

Identifiants

pubmed: 32244541
pii: cells9040848
doi: 10.3390/cells9040848
pmc: PMC7226741
pii:
doi:

Substances chimiques

acid sphingomyelinase-1 EC 3.1.4.-
Sphingomyelin Phosphodiesterase EC 3.1.4.12
GTP Phosphohydrolases EC 3.6.1.-
Mfn1 protein, mouse EC 3.6.1.-
Opa1 protein, mouse EC 3.6.1.-

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Déclaration de conflit d'intérêts

The authors declare no competing financial interests.

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Auteurs

Marco Coazzoli (M)

Department of Biomedical and Clinical Sciences "Luigi Sacco" (DIBIC), Università degli Studi di Milano, 20157 Milano, Italy.

Alessandra Napoli (A)

Department of Biomedical and Clinical Sciences "Luigi Sacco" (DIBIC), Università degli Studi di Milano, 20157 Milano, Italy.
Unit of Clinical Pharmacology, University Hospital "Luigi Sacco"-ASST Fatebenefratelli Sacco, 20157 Milano, Italy.

Paulina Roux-Biejat (P)

Department of Biomedical and Clinical Sciences "Luigi Sacco" (DIBIC), Università degli Studi di Milano, 20157 Milano, Italy.

Clara De Palma (C)

Department of Medical Biotechnology and Translational Medicine (BIOMETRA), Università degli Studi di Milano, 20129 Milano, Italy.

Claudia Moscheni (C)

Department of Biomedical and Clinical Sciences "Luigi Sacco" (DIBIC), Università degli Studi di Milano, 20157 Milano, Italy.

Elisabetta Catalani (E)

Department for Innovation in Biological, Agro-food and Forest systems (DIBAF), Università degli Studi della Tuscia, 01100 Viterbo, Italy.

Silvia Zecchini (S)

Department of Biomedical and Clinical Sciences "Luigi Sacco" (DIBIC), Università degli Studi di Milano, 20157 Milano, Italy.

Vincenzo Conte (V)

Department of Biomedical Sciences for Health (SCIBIS), Università degli Studi di Milano, 20133 Milano, Italy.

Matteo Giovarelli (M)

Department of Biomedical and Clinical Sciences "Luigi Sacco" (DIBIC), Università degli Studi di Milano, 20157 Milano, Italy.

Sonia Caccia (S)

Department of Biomedical and Clinical Sciences "Luigi Sacco" (DIBIC), Università degli Studi di Milano, 20157 Milano, Italy.

Patrizia Procacci (P)

Department of Biomedical Sciences for Health (SCIBIS), Università degli Studi di Milano, 20133 Milano, Italy.

Davide Cervia (D)

Department for Innovation in Biological, Agro-food and Forest systems (DIBAF), Università degli Studi della Tuscia, 01100 Viterbo, Italy.

Emilio Clementi (E)

Department of Biomedical and Clinical Sciences "Luigi Sacco" (DIBIC), Università degli Studi di Milano, 20157 Milano, Italy.
Scientific Institute IRCCS "Eugenio Medea", 23842 Bosisio Parini, Italy.

Cristiana Perrotta (C)

Department of Biomedical and Clinical Sciences "Luigi Sacco" (DIBIC), Università degli Studi di Milano, 20157 Milano, Italy.

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Classifications MeSH