A Chinese Boy With Lupus Anticoagulant-hypoprothrombinemia Syndrome: A Case Report and Review of the Literature.


Journal

Journal of pediatric hematology/oncology
ISSN: 1536-3678
Titre abrégé: J Pediatr Hematol Oncol
Pays: United States
ID NLM: 9505928

Informations de publication

Date de publication:
01 04 2021
Historique:
received: 08 11 2019
accepted: 19 03 2020
pubmed: 15 4 2020
medline: 20 5 2021
entrez: 15 4 2020
Statut: ppublish

Résumé

We herein report an unusual case of lupus with bleeding diathesis in a Chinese adolescent boy. In the presence of lupus anticoagulant and hypoprothrombinemia, the diagnosis of lupus anticoagulant-hypoprothrombinemia syndrome was made. He responded promptly to immunosuppressive agents and achieved disease remission.

Identifiants

pubmed: 32287097
pii: 00043426-202104000-00038
doi: 10.1097/MPH.0000000000001805
doi:

Substances chimiques

Blood Coagulation Factors 0
Lupus Coagulation Inhibitor 0

Types de publication

Case Reports Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

e445-e447

Informations de copyright

Copyright © 2020 Wolters Kluwer Health, Inc. All rights reserved.

Déclaration de conflit d'intérêts

The authors declare no conflict of interest.

Références

Miyakis S, Lockshin MD, Atsumi T, et al. International consensus statement on an update of the classification criteria for definite antiphospholipid syndrome (APS). J Thromb Haemost. 2006;4:295–306.
Chung CH, Park CY. Lupus anticoagulant-hypoprothrombinemia in healthy adult. Korean J Intern Med. 2008;23:149–151.
Mulliez S, De Keyser F, Verbist C, et al. Lupus anticoagulant-hypoprothrombinemia syndrome: report of two cases and review of the literature. Lupus. 2014;24:736–745.
Erkan D, Bateman H, Lockshin M. Lupus anticoagulant-hypoprothrombinemia syndrome associated with systemic lupus erythematosus: report of 2 cases and review of literature. Lupus. 1999;8:560–564.
Mazodier K, Arnaud L, Mathian A, et al. Lupus anticoagulant-hypoprothrombinemia syndrome: report of 8 cases and review of the literature. Medicine. 2012;91:251–260.
Vivaldi P, Rossetti G, Galli M, et al. Severe bleeding due to acquired hypoprothrombinemia-lupus anticoagulant syndrome. Case report and review of literature. Haematologica. 1997;82:345–347.
Rapaport SI, Ames SB, Duvall BJ. A plasma coagulation defect in systemic lupus erythematosus arising from hypoprothrombinemia combined with antiprothrombinase activity. Blood. 1960;15:212–227.
Sarker T, Roy S, Hollon W, et al. Lupus anticoagulant acquired hypoprothrombinemia syndrome in childhood: two distinct patterns and review of the literature. Haemophilia. 2015;21:754–760.
Kim JS, Kim MJ, Bae EY, et al. Pulmonary hemorrhage in pediatric lupus anticoagulant hypoprothrombinemia syndrome. Korean J Pediatr. 2014;57:202–205.
Baudo F, Redaelli R, Pezzetti L, et al. Prothrombin-antibody coexistent with lupus anticoagulant (LA): clinical study and immunochemical characterization. Thromb Res. 1990;57:279–287.
Vinet E, Rich E, Senécal J-L. Thromboembolism complicating the treatment of lupus anticoagulant hypoprothrombinemia syndrome. J Rheumatol. 2006;33:2088–2090.
Knobe K, Tedgård U, Ek T, et al. Lupus anticoagulants in two children—bleeding due to nonphospholipid-dependent antiprothrombin antibodies. Eur J Pediatr. 2012;171:1383–1387.

Auteurs

Eugene Yu-Hin Chan (EY)

Departments of Paediatrics.

Kate F S Leung (KFS)

Pathology, Princess Margaret Hospital, Hong Kong.

Euan T L Soo (ETL)

Departments of Paediatrics.

Alison L T Ma (ALT)

Departments of Paediatrics.

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Classifications MeSH