The safety and efficacy of mycophenolate mofetil in children and adolescents with steroid-dependent nephrotic syndrome: a single-centre study.

MMF nephrotic syndrome steroid-dependent

Journal

Clinical kidney journal
ISSN: 2048-8505
Titre abrégé: Clin Kidney J
Pays: England
ID NLM: 101579321

Informations de publication

Date de publication:
Apr 2020
Historique:
received: 23 09 2018
accepted: 15 04 2019
entrez: 17 4 2020
pubmed: 17 4 2020
medline: 17 4 2020
Statut: epublish

Résumé

Steroid-dependent nephrotic syndrome (SDNS) patients experience frequent relapse or adverse effects on long-term treatment with steroids or cyclophosphamide. This study assessed the efficacy and side effect profile of mycophenolate mofetil (MMF) therapy in children with nephrotic syndrome in our population. A retrospective study was performed on children with SDNS who were on MMF therapy for a minimum period of 1 year, and were on regular follow-up in the Department of Nephrology at the Institute of Child Health and hospital for children attached to Madras Medical College. The study included 87 patients, with a male:female ratio of 2:1. The median age at diagnosis of nephrotic syndrome was 3 years [95% confidence interval (CI): 1-8 years], which was found to be a statistically significant risk factor for MMF failure. The median duration of follow-up after initiation of MMF therapy was 3 years and 3 months (95% CI: 1 year and 3 months to 6 years and 6 months). At initial evaluation, 31 (36%) patients presented with SDNS while the remaining had frequently relapsing nephrotic syndrome progressing to SDNS. Intravenous cyclophosphamide was used as first-line therapy in 82 patients, of whom 24 patients had persistent proteinuria while the remaining 58 had attained remission for a median duration of 6 months. The median duration of treatment with MMF was 2 years and 6 months (95% CI: 1 year and 3 months to 4 years and 6 months). MMF was used at a mean dose of 28.5 mg/kg. Seventy-two (83%) patients were MMF-sensitive, and these patients had a reduction in mean prednisolone dose from 1.28 to 0.35 mg/kg (P < 0.05). Among the MMF-sensitive patients, 31 had stopped MMF after a minimum period of 2 years, following which they had a median remission period of 5 months (95% CI: 1-8 months). MMF failure occurred in 15 (17%) patients. Adverse events were documented in 19 (22%) patients. Continuous MMF therapy achieved remission in 83% of patients. MMF was well tolerated in the study population and discontinuation of MMF resulted in 100% relapse.

Sections du résumé

BACKGROUND BACKGROUND
Steroid-dependent nephrotic syndrome (SDNS) patients experience frequent relapse or adverse effects on long-term treatment with steroids or cyclophosphamide. This study assessed the efficacy and side effect profile of mycophenolate mofetil (MMF) therapy in children with nephrotic syndrome in our population.
METHODS METHODS
A retrospective study was performed on children with SDNS who were on MMF therapy for a minimum period of 1 year, and were on regular follow-up in the Department of Nephrology at the Institute of Child Health and hospital for children attached to Madras Medical College.
RESULTS RESULTS
The study included 87 patients, with a male:female ratio of 2:1. The median age at diagnosis of nephrotic syndrome was 3 years [95% confidence interval (CI): 1-8 years], which was found to be a statistically significant risk factor for MMF failure. The median duration of follow-up after initiation of MMF therapy was 3 years and 3 months (95% CI: 1 year and 3 months to 6 years and 6 months). At initial evaluation, 31 (36%) patients presented with SDNS while the remaining had frequently relapsing nephrotic syndrome progressing to SDNS. Intravenous cyclophosphamide was used as first-line therapy in 82 patients, of whom 24 patients had persistent proteinuria while the remaining 58 had attained remission for a median duration of 6 months. The median duration of treatment with MMF was 2 years and 6 months (95% CI: 1 year and 3 months to 4 years and 6 months). MMF was used at a mean dose of 28.5 mg/kg. Seventy-two (83%) patients were MMF-sensitive, and these patients had a reduction in mean prednisolone dose from 1.28 to 0.35 mg/kg (P < 0.05). Among the MMF-sensitive patients, 31 had stopped MMF after a minimum period of 2 years, following which they had a median remission period of 5 months (95% CI: 1-8 months). MMF failure occurred in 15 (17%) patients. Adverse events were documented in 19 (22%) patients.
CONCLUSIONS CONCLUSIONS
Continuous MMF therapy achieved remission in 83% of patients. MMF was well tolerated in the study population and discontinuation of MMF resulted in 100% relapse.

Identifiants

pubmed: 32296522
doi: 10.1093/ckj/sfz061
pii: sfz061
pmc: PMC7147304
doi:

Types de publication

Journal Article

Langues

eng

Pagination

179-183

Informations de copyright

© The Author(s) 2019. Published by Oxford University Press on behalf of ERA-EDTA.

Références

Pediatr Nephrol. 2012 Mar;27(3):389-96
pubmed: 21947272
Pediatr Nephrol. 2005 Sep;20(9):1265-8
pubmed: 15942779
Pediatr Nephrol. 2007 Dec;22(12):2059-65
pubmed: 17938973
Pediatr Nephrol. 2001 Mar;16(3):271-82
pubmed: 11322378
Clin J Am Soc Nephrol. 2006 Nov;1(6):1173-8
pubmed: 17699344
Kidney Int. 2001 May;59(5):1919-27
pubmed: 11318964
Pediatr Nephrol. 2013 Jan;28(1):93-7
pubmed: 22890513
Cochrane Database Syst Rev. 2008 Jan 23;(1):CD002290
pubmed: 18254005
Kidney Int Suppl (2011). 2012 Jun;2(2):163-171
pubmed: 25028636
Immunol Rev. 1993 Dec;136:5-28
pubmed: 7907572
Clin Kidney J. 2013 Aug;6(4):384-9
pubmed: 27293565
Arch Dis Child. 2000 Jul;83(1):45-51
pubmed: 10868999

Auteurs

Saravanakumar Karunamoorthy (S)

Institute of Nephrology, Madras Medical College, Chennai, India.

Dineshkumar Thanigachalam (D)

Institute of Nephrology, Madras Medical College, Chennai, India.

Dhanapriya Jeyachandran (D)

Institute of Nephrology, Madras Medical College, Chennai, India.

Sakthirajan Ramanathan (S)

Institute of Nephrology, Madras Medical College, Chennai, India.

Gopalakrishnan Natarajan (G)

Institute of Nephrology, Madras Medical College, Chennai, India.

Balasubramaniam Thoppalan (B)

Institute of Nephrology, Madras Medical College, Chennai, India.

Classifications MeSH