Bcl11 Transcription Factors Regulate Cortical Development and Function.
Bcl11a
Bcl11b
brain development
hippocampus
neocortex
neural circuitry
neurological disorders
transcription factors
Journal
Frontiers in molecular neuroscience
ISSN: 1662-5099
Titre abrégé: Front Mol Neurosci
Pays: Switzerland
ID NLM: 101477914
Informations de publication
Date de publication:
2020
2020
Historique:
received:
22
01
2020
accepted:
11
03
2020
entrez:
24
4
2020
pubmed:
24
4
2020
medline:
24
4
2020
Statut:
epublish
Résumé
Transcription factors regulate multiple processes during brain development and in the adult brain, from brain patterning to differentiation and maturation of highly specialized neurons as well as establishing and maintaining the functional neuronal connectivity. The members of the zinc-finger transcription factor family Bcl11 are mainly expressed in the hematopoietic and central nervous systems regulating the expression of numerous genes involved in a wide range of pathways. In the brain Bcl11 proteins are required to regulate progenitor cell proliferation as well as differentiation, migration, and functional integration of neural cells. Mutations of the human Bcl11 genes lead to anomalies in multiple systems including neurodevelopmental impairments like intellectual disabilities and autism spectrum disorders.
Identifiants
pubmed: 32322190
doi: 10.3389/fnmol.2020.00051
pmc: PMC7158892
doi:
Types de publication
Journal Article
Review
Langues
eng
Pagination
51Informations de copyright
Copyright © 2020 Simon, Wiegreffe and Britsch.
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