Successful Preclinical Development of Gene Therapy for Recombinase-Activating Gene-1-Deficient SCID.

B lymphocytes CD34+ cells RAG1 SCID T lymphocytes gene rearrangement gene therapy lentiviral vector

Journal

Molecular therapy. Methods & clinical development
ISSN: 2329-0501
Titre abrégé: Mol Ther Methods Clin Dev
Pays: United States
ID NLM: 101624857

Informations de publication

Date de publication:
12 Jun 2020
Historique:
received: 13 03 2020
accepted: 23 03 2020
entrez: 24 4 2020
pubmed: 24 4 2020
medline: 24 4 2020
Statut: epublish

Résumé

Recombinase-activating gene-1 (RAG1)-deficient severe combined immunodeficiency (SCID) patients lack B and T lymphocytes due to the inability to rearrange immunoglobulin and T cell receptor genes. Gene therapy is an alternative for those RAG1-SCID patients who lack a suitable bone marrow donor. We designed lentiviral vectors with different internal promoters driving codon-optimized

Identifiants

pubmed: 32322605
doi: 10.1016/j.omtm.2020.03.016
pii: S2329-0501(20)30046-2
pmc: PMC7163047
doi:

Types de publication

Journal Article

Langues

eng

Pagination

666-682

Informations de copyright

© 2020 The Authors.

Références

Blood. 2018 Oct 25;132(17):1737-1749
pubmed: 30154114
J Virol. 2012 Sep;86(17):9088-95
pubmed: 22696657
Lancet. 2004 Dec 18-31;364(9452):2181-7
pubmed: 15610804
J Virol. 1998 Nov;72(11):8463-71
pubmed: 9765382
Blood. 2006 Jan 1;107(1):63-72
pubmed: 16174758
Curr Opin Mol Ther. 2002 Oct;4(5):515-22
pubmed: 12435054
J Allergy Clin Immunol. 2017 Mar;139(3):726-732
pubmed: 28270364
J Clin Invest. 2007 May;117(5):1260-9
pubmed: 17476358
Nat Immunol. 2010 Jun;11(6):457-60
pubmed: 20485269
Science. 2000 Apr 28;288(5466):669-72
pubmed: 10784449
Bioinformatics. 2019 Oct 30;:
pubmed: 31665245
Blood. 1999 Nov 15;94(10):3349-57
pubmed: 10552944
J Allergy Clin Immunol. 2010 Sep;126(3):602-10.e1-11
pubmed: 20673987
Sci Transl Med. 2016 Apr 20;8(335):335ra57
pubmed: 27099176
J Exp Med. 2005 Jun 6;201(11):1715-23
pubmed: 15928199
N Engl J Med. 2009 Jan 29;360(5):447-58
pubmed: 19179314
J Clin Invest. 2007 Jun;117(6):1456-65
pubmed: 17549248
Blood. 2009 Mar 26;113(13):2965-75
pubmed: 19126872
Nature. 2006 Sep 21;443(7109):E5; discussion E6-7
pubmed: 16988660
Blood. 2002 Sep 15;100(6):2145-52
pubmed: 12200379
J Vis Exp. 2014 Jun 25;(88):e51543
pubmed: 24998871
Leukemia. 2011 Sep;25(9):1471-83
pubmed: 21617701
Nat Rev Cancer. 2003 Jul;3(7):477-88
pubmed: 12835668
Biores Open Access. 2014 Jun 1;3(3):110-6
pubmed: 24940562
Leukemia. 2003 Dec;17(12):2257-317
pubmed: 14671650
Stem Cells. 2012 Aug;30(8):1771-80
pubmed: 22689616
Blood. 2006 Oct 15;108(8):2545-53
pubmed: 16825499
J Clin Invest. 2007 May;117(5):1270-81
pubmed: 17476359
J Clin Invest. 2008 Sep;118(9):3143-50
pubmed: 18688286
Mol Ther. 2008 Mar;16(3):590-8
pubmed: 18180772
J Allergy Clin Immunol. 2016 Feb;137(2):517-526.e3
pubmed: 26441229
Science. 2009 Nov 6;326(5954):818-23
pubmed: 19892975
Front Pediatr. 2019 Oct 31;7:443
pubmed: 31737588
Blood Cells Mol Dis. 2011 Jun 15;47(1):72-8
pubmed: 21531153
Hum Gene Ther. 2016 Feb;27(2):108-16
pubmed: 26790362
Mol Ther. 2007 Nov;15(11):1910-6
pubmed: 17726455
Nature. 2010 Sep 16;467(7313):318-22
pubmed: 20844535
Expert Opin Biol Ther. 2008 Apr;8(4):397-407
pubmed: 18352845
Mol Ther. 2008 Aug;16(8):1490-9
pubmed: 18560421
J Allergy Clin Immunol. 2009 Dec;124(6):1152-60.e12
pubmed: 20004776
JAMA. 2006 Feb 1;295(5):508-18
pubmed: 16449616
Mol Ther Methods Clin Dev. 2018 Aug 08;10:341-347
pubmed: 30191160
Mol Ther. 2008 Feb;16(2):396-403
pubmed: 18223550
Proc Natl Acad Sci U S A. 1993 May 1;90(9):4319-23
pubmed: 8483950
Cell Stem Cell. 2017 Nov 2;21(5):574-590
pubmed: 29100011
Hum Gene Ther. 2006 Mar;17(3):253-63
pubmed: 16544975
Blood. 2015 Jun 4;125(23):3563-9
pubmed: 25869287
Expert Opin Biol Ther. 2005 Sep;5(9):1175-82
pubmed: 16120048
Blood. 2006 Nov 1;108(9):2979-88
pubmed: 16835374
Science. 2003 Oct 17;302(5644):415-9
pubmed: 14564000
Clin Dev Immunol. 2012;2012:467101
pubmed: 22474479
N Engl J Med. 2017 Oct 26;377(17):1630-1638
pubmed: 28976817
J Clin Invest. 2009 Apr;119(4):964-75
pubmed: 19307726
J Allergy Clin Immunol. 2014 Jul;134(1):242-3
pubmed: 25117803
Nucleosides Nucleotides Nucleic Acids. 2004 Oct;23(8-9):1245-8
pubmed: 15571238
Blood. 2018 Jul 19;132(3):281-292
pubmed: 29743177
J Allergy Clin Immunol. 2014 Apr;133(4):1116-23
pubmed: 24332219
J Clin Invest. 2007 Aug;117(8):2233-40
pubmed: 17671653

Auteurs

Laura Garcia-Perez (L)

Department of Immunohematology and Blood Transfusion, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Marja van Eggermond (M)

Department of Immunohematology and Blood Transfusion, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Lieke van Roon (L)

Department of Immunohematology and Blood Transfusion, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Sandra A Vloemans (SA)

Department of Immunohematology and Blood Transfusion, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Martijn Cordes (M)

Department of Immunohematology and Blood Transfusion, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Axel Schambach (A)

Institute of Experimental Hematology, Hannover Medical School, 30625 Hannover, Germany.

Michael Rothe (M)

Institute of Experimental Hematology, Hannover Medical School, 30625 Hannover, Germany.

Dagmar Berghuis (D)

Willem-Alexander Children's Hospital Department of Pediatrics, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Chantal Lagresle-Peyrou (C)

Biotherapy Clinical Investigation Center, Groupe Hospitalier Universitaire Ouest, Assistance Publique-Hôpitaux de Paris, INSERM CIC 1416, Paris, France.
Laboratory of Human Lymphohematopoiesis, INSERM UMR 1163, Imagine Institute and Paris Descartes University-Sorbonne Paris Cité, 75015 Paris, France.
Department of Biotherapy, Necker Children's Hospital, Assistance Publique-Hôpitaux de Paris, 75015 Paris, France.

Marina Cavazzana (M)

Biotherapy Clinical Investigation Center, Groupe Hospitalier Universitaire Ouest, Assistance Publique-Hôpitaux de Paris, INSERM CIC 1416, Paris, France.
Laboratory of Human Lymphohematopoiesis, INSERM UMR 1163, Imagine Institute and Paris Descartes University-Sorbonne Paris Cité, 75015 Paris, France.
Department of Biotherapy, Necker Children's Hospital, Assistance Publique-Hôpitaux de Paris, 75015 Paris, France.

Fang Zhang (F)

Molecular and Cellular Immunology, Great Ormond Street Institute of Child Health, and Great Ormond Street Hospital NHS Trust, London WC1N 1EH, UK.

Adrian J Thrasher (AJ)

Molecular and Cellular Immunology, Great Ormond Street Institute of Child Health, and Great Ormond Street Hospital NHS Trust, London WC1N 1EH, UK.

Daniela Salvatori (D)

Central Laboratory Animal Facility, Pathology Unit, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.
Department of Pharmacy, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.
Pathogenesis and Treatment of Immune and Bone Diseases Unit, San Raffaele Telethon Institute for Gene Therapy (SR-Tiget), IRCCS San Raffaele Scientific Institute, 20132 Milan, Italy.
Anatomy and Physiology Division, Clinical Sciences, Faculty of Veterinary Medicine, Utrecht University, Yalelaan1, 3584CL Utrecht, the Netherlands.

Pauline Meij (P)

Department of Pharmacy, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Anna Villa (A)

Pathogenesis and Treatment of Immune and Bone Diseases Unit, San Raffaele Telethon Institute for Gene Therapy (SR-Tiget), IRCCS San Raffaele Scientific Institute, 20132 Milan, Italy.

Jacques J M Van Dongen (JJM)

Department of Immunohematology and Blood Transfusion, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Jaap-Jan Zwaginga (JJ)

Department of Immunohematology and Blood Transfusion, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Mirjam van der Burg (M)

Willem-Alexander Children's Hospital Department of Pediatrics, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

H Bobby Gaspar (HB)

Molecular and Cellular Immunology, Great Ormond Street Institute of Child Health, and Great Ormond Street Hospital NHS Trust, London WC1N 1EH, UK.

Arjan Lankester (A)

Willem-Alexander Children's Hospital Department of Pediatrics, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Frank J T Staal (FJT)

Department of Immunohematology and Blood Transfusion, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Karin Pike-Overzet (K)

Department of Immunohematology and Blood Transfusion, Leiden University Medical Center, 2333ZA Leiden, the Netherlands.

Classifications MeSH