Marfan Syndrome Versus Bicuspid Aortic Valve Disease: Comparative Analysis of Obstetric Outcome and Pregnancy-Associated Immediate and Long-Term Aortic Complications.

Marfan syndrome aortic dissection aortopathy bicuspid aortic valve pregnancy

Journal

Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588

Informations de publication

Date de publication:
15 Apr 2020
Historique:
received: 13 03 2020
revised: 10 04 2020
accepted: 11 04 2020
entrez: 25 4 2020
pubmed: 25 4 2020
medline: 25 4 2020
Statut: epublish

Résumé

Pregnancy poses a threat to women with aortopathy. Conclusive data on the obstetric and aortic outcome in this risk collective, especially when it comes to aortic complications in the long term, are still missing. This study offers a comparative analysis of pregnancy-associated outcome in 113 consecutive women with Marfan syndrome or bicuspid aortic valve disease, including 46 ever-pregnant and 37 never-pregnant women with Marfan syndrome, and 23 ever-pregnant and 7 never-pregnant females with bicuspid aortic valve disease. The overall obstetric outcome was comparable between ever-pregnant women with Marfan syndrome and with bicuspid aortic valve disease (

Identifiants

pubmed: 32326432
pii: jcm9041124
doi: 10.3390/jcm9041124
pmc: PMC7230569
pii:
doi:

Types de publication

Journal Article

Langues

eng

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Auteurs

Betül Toprak (B)

Department of Cardiology, University Heart and Vascular Center Hamburg, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Katalin Szöcs (K)

Department of Cardiology, University Heart and Vascular Center Hamburg, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Elvin Zengin-Sahm (E)

Department of Cardiology, University Heart and Vascular Center Hamburg, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Christoph Sinning (C)

Department of Cardiology, University Heart and Vascular Center Hamburg, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Amra Hot (A)

Department of Medical Biometry and Epidemiology, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Peter Bannas (P)

Department of Diagnostic and Interventional Radiology, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Kurt Hecher (K)

Department of Obstetrics and Fetal Medicine, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Bernd Hüneke (B)

Department of Obstetrics and Fetal Medicine, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Thomas S Mir (TS)

Department of Pediatric Cardiology, University Heart and Vascular Center Hamburg, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Meike Rybczynski (M)

Department of Cardiology, University Heart and Vascular Center Hamburg, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Evaldas Girdauskas (E)

Department of Cardiovascular Surgery, University Heart and Vascular Center Hamburg, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Stefan Blankenberg (S)

Department of Cardiology, University Heart and Vascular Center Hamburg, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Yskert von Kodolitsch (Y)

Department of Cardiology, University Heart and Vascular Center Hamburg, University Medical Center Hamburg-Hospital Eppendorf, 20246 Hamburg, Germany.

Classifications MeSH