Long-Term Safety and Efficacy of Nonacog Beta Pegol (N9-GP) Administered for at Least 5 Years in Previously Treated Children with Hemophilia B.


Journal

Thrombosis and haemostasis
ISSN: 2567-689X
Titre abrégé: Thromb Haemost
Pays: Germany
ID NLM: 7608063

Informations de publication

Date de publication:
May 2020
Historique:
entrez: 6 5 2020
pubmed: 6 5 2020
medline: 25 8 2020
Statut: ppublish

Résumé

Long-term safety and efficacy data of extended half-life factor IX (FIX) prophylaxis in children with hemophilia B (HB) are sparse. paradigm 5 is a multinational, open-label, single-arm, phase III trial assessing once-weekly (40 IU/kg) prophylactic nonacog beta pegol (N9-GP) in previously treated patients (PTPs) aged ≤ 12 years with HB (FIX activity ≤ 2%). Primary endpoint: incidence of anti-FIX inhibitory antibodies (≥ 0.6 Bethesda Units). We present a 5-year analysis (

Identifiants

pubmed: 32369845
doi: 10.1055/s-0040-1709521
doi:

Substances chimiques

Hemostatics 0
Recombinant Proteins 0
nonacog beta pegol 27Y83O992Q
Polyethylene Glycols 3WJQ0SDW1A
Factor IX 9001-28-9

Types de publication

Clinical Trial, Phase III Journal Article Multicenter Study

Langues

eng

Sous-ensembles de citation

IM

Pagination

737-746

Informations de copyright

Georg Thieme Verlag KG Stuttgart · New York.

Déclaration de conflit d'intérêts

M.C. has received grant/research support from: Baxalta (Shire), Bayer, Biogen, Novo Nordisk and Pfizer, has been a consultant for Baxalta/Shire/Takeda, Bayer, Biogen/Bioverativ/Sanofi, CSL Behring, Grifols, Novo Nordisk, Octapharma, Pfizer, and Roche, and is a member of speaker bureaus of Baxalta (Shire), Bayer, Biogen, CSL Behring, Grifols, Novo Nordisk, Octapharma, Pfizer, and Roche.S.K. has received grant/research support from: local principal investigator (PI) research funding for Bayer, Bioverativ, Daiichi Sankyo, Grifols, and Novo Nordisk, and is a member of speaker bureaus/advisory boards for Bayer, Bioverativ, and Novo Nordisk.M.Y.L. has no conflict of interest.M.T. has served on advisory boards for Bayer, Bioverativ, Chugai, and Novo Nordisk; has received research support in clinical trials as a local PI for Bioverativ, Chugai, CSL Behring, and Novo Nordisk, and has received speaker's fees from Bayer, Bioverativ, Chugai, CSL Behring, Novo Nordisk, and Shire.D.R. and C.S. are employees of Novo Nordisk A/S, Søborg, Denmark.E.S. has served on advisory boards for Bayer, Bioverativ, CSL Behring, Grifols, Kedrion, Novo Nordisk, Octapharma, Pfizer, Roche, Shire/Takeda, SOBI, Spark, and Uniqure and has been a member of speaker bureaus for Bayer, CSL Behring, Grifols, Kedrion, Novo Nordisk, Pfizer, Roche, Shire/Takeda, and SOBI.

Auteurs

Manuel Carcao (M)

Division of Haematology/Oncology, Department of Paediatrics and Child Health Evaluative Sciences, Research Institute, Hospital for Sick Children, University of Toronto, Toronto, Ontario, Canada.

Susan Kearney (S)

Center for Bleeding and Clotting Disorders, Children's Hospital of Minnesota, Minneapolis, Minnesota, United States.

Meng Yao Lu (MY)

Department of Pediatrics, National Taiwan University Hospital, Taipei, Taiwan.

Masashi Taki (M)

Department of Pediatrics, Yokohama City Seibu Hospital, St. Marianna University School of Medicine, Yokohama, Japan.

Daniel Rubens (D)

Novo Nordisk A/S, Søborg, Denmark.

Chunduo Shen (C)

Novo Nordisk A/S, Søborg, Denmark.

Elena Santagostino (E)

Foundation IRCCS Cá Granda, Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Maggiore Hospital Policlinico, Milan, Italy.

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Classifications MeSH