Systemic Redox Imbalance in Patients with Chronic Granulomatous Disease.

antioxidants chronic granulomatous disease coenzyme Q10 oxidative stress primary immunodeficiency

Journal

Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588

Informations de publication

Date de publication:
09 May 2020
Historique:
received: 06 04 2020
revised: 04 05 2020
accepted: 07 05 2020
entrez: 14 5 2020
pubmed: 14 5 2020
medline: 14 5 2020
Statut: epublish

Résumé

The aim of our study was to evaluate redox status, enzymatic and non-enzymatic antioxidant barriers, oxidative damage of proteins, lipids and DNA, as well as concentration of coenzyme Q10 and vitamins A and E in patients with chronic granulomatous disease (CGD). The study was performed on fifteen Caucasian individuals (median age 24 years and seven months) diagnosed with CGD. The mutation in the

Identifiants

pubmed: 32397350
pii: jcm9051397
doi: 10.3390/jcm9051397
pmc: PMC7290492
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : Uniwersytet Medyczny w Bialymstoku
ID : SUB/1/DN/19/002/1126

Références

Nat Protoc. 2010 Jan;5(1):51-66
pubmed: 20057381
Methodist Debakey Cardiovasc J. 2019 Jul-Sep;15(3):185-191
pubmed: 31687097
Oxid Med Cell Longev. 2017;2017:6501046
pubmed: 28698768
Eur J Pediatr. 2020 May;179(5):689-697
pubmed: 32162064
Adv Ther. 2017 Dec;34(12):2543-2557
pubmed: 29168144
Curr Opin Immunol. 2004 Feb;16(1):42-7
pubmed: 14734109
Int J Mol Sci. 2010 Nov 17;11(11):4631-59
pubmed: 21151461
Clin Infect Dis. 2015 Apr 15;60(8):1176-83
pubmed: 25537876
J Med Food. 2016 Mar;19(3):238-44
pubmed: 26872287
Immunol Res. 2018 Feb;66(1):158-171
pubmed: 29185130
Circulation. 2009 Oct 20;120(16):1616-22
pubmed: 19805647
Sci Rep. 2019 Jan 28;9(1):793
pubmed: 30692599
J Lab Clin Med. 1967 Jul;70(1):158-69
pubmed: 6066618
J Cell Physiol. 2002 Jul;192(1):1-15
pubmed: 12115731
Medicine (Baltimore). 2000 May;79(3):155-69
pubmed: 10844935
Nat Med. 2016 Feb;22(2):146-53
pubmed: 26779811
Physiol Res. 2002;51(6):597-604
pubmed: 12511184
Oxid Med Cell Longev. 2017;2017:4590127
pubmed: 29430280
J Pathol. 2018 Nov;246(3):300-310
pubmed: 30062795
Mol Syndromol. 2014 Jul;5(3-4):163-9
pubmed: 25126049
Int J Biochem Cell Biol. 2007;39(1):44-84
pubmed: 16978905
J Biol Chem. 1972 May 25;247(10):3170-5
pubmed: 4623845
J Pharm Biomed Anal. 2006 Sep 18;42(2):232-6
pubmed: 16765550
Oxid Med Cell Longev. 2018 Sep 6;2018:6940515
pubmed: 30271528
Blood. 2010 Sep 2;116(9):1570-3
pubmed: 20495074
J Pediatric Infect Dis Soc. 2018 May 9;7(suppl_1):S18-S24
pubmed: 29746679
Antioxid Redox Signal. 2008 Oct;10(10):1699-712
pubmed: 18576917
Arch Biochem Biophys. 1999 Jan 15;361(2):252-6
pubmed: 9882453
Oxid Med Cell Longev. 2019 Jul 4;2019:2606120
pubmed: 31354904
Int J Mol Sci. 2019 Feb 18;20(4):
pubmed: 30781611
J Cell Mol Med. 2010 Apr;14(4):840-60
pubmed: 19754673
Oxid Med Cell Longev. 2014;2014:572491
pubmed: 24868314
Front Immunol. 2019 Sep 27;10:2322
pubmed: 31611883
Free Radic Biol Med. 2018 Sep;125:44-52
pubmed: 29953922
J Med Food. 2017 Sep;20(9):821-829
pubmed: 28816577
Oxid Med Cell Longev. 2019 Dec 5;2019:4393460
pubmed: 31885792
Biomolecules. 2019 Oct 22;9(10):
pubmed: 31652642
Free Radic Biol Med. 2017 Oct;111:316-327
pubmed: 28456642
J Am Heart Assoc. 2014 Jun 27;3(3):e000920
pubmed: 24973227
Mol Cells. 2010 Nov;30(5):383-91
pubmed: 21113821
Free Radic Biol Med. 1998 Nov 1;25(7):839-47
pubmed: 9823550
Biochem Med (Zagreb). 2012;22(1):63-75
pubmed: 22384520
Free Radic Res. 2019 Aug;53(8):841-850
pubmed: 31234658
Front Immunol. 2017 Dec 21;8:1828
pubmed: 29375548
Environ Mol Mutagen. 2017 Jun;58(5):235-263
pubmed: 28485537
J Allergy Clin Immunol. 2017 May;139(5):1641-1649.e6
pubmed: 27702670
J Allergy Clin Immunol. 2016 Aug;138(2):375-85
pubmed: 27262745
Biomolecules. 2019 Dec 15;9(12):
pubmed: 31847462
CNS Neurosci Ther. 2017 Feb;23(2):188-189
pubmed: 28052569
Methods Enzymol. 1984;105:121-6
pubmed: 6727660

Auteurs

Edyta Heropolitanska-Pliszka (E)

Clinical Immunology the Children's Memorial Health Institute, al. Dzieci Polskich 20, 04-730 Warsaw, Poland.

Klaudia Berk (K)

Department of Physiology, Medical University of Bialystok, ul. Mickiewicza 2c, 15-233 Bialystok, Poland.

Mateusz Maciejczyk (M)

Department of Hygiene, Epidemiology and Ergonomics, Medical University of Bialystok, ul. Mickiewicza 2c, 15-233 Bialystok, Poland.

Jolanta Sawicka-Powierza (J)

Department of Family Medicine, Medical University of Bialystok, 15-054 Bialystok, Poland.

Ewa Bernatowska (E)

Clinical Immunology the Children's Memorial Health Institute, al. Dzieci Polskich 20, 04-730 Warsaw, Poland.

Beata Wolska-Kusnierz (B)

Clinical Immunology the Children's Memorial Health Institute, al. Dzieci Polskich 20, 04-730 Warsaw, Poland.

Malgorzata Pac (M)

Clinical Immunology the Children's Memorial Health Institute, al. Dzieci Polskich 20, 04-730 Warsaw, Poland.

Nel Dabrowska-Leonik (N)

Clinical Immunology the Children's Memorial Health Institute, al. Dzieci Polskich 20, 04-730 Warsaw, Poland.

Barbara Piatosa (B)

Histocompatibility Laboratory, Children's Memorial Health Institute, al. Dzieci Polskich 20, 04-730 Warsaw, Poland.

Aleksandra Lewandowicz-Uszynska (A)

3rd Department and Clinic of Pediatrics, Immunology and Rheumatology of Developmental Age, Wroclaw Medical University, ul. Koszarowa 5, 50-367 Wrocław, Poland.

Joanna Karpinska (J)

Institute of Chemistry, University of Bialystok, ul. Ciołkowskiego. 1K, 15-245 Białystok, Poland.

Anna Zalewska (A)

Experimental Dentistry Laboratory, Medical University of Bialystok, ul. Szpitalna 37, 15-295 Bialystok, Poland.

Bozena Mikoluc (B)

Department of Pediatrics, Rheumatology, Immunology and Metabolic Bone Diseases, Waszyngtona 17, 15-274 Bialystok, Poland.

Classifications MeSH