Verification of Underlying Genetic Cause in a Cohort of Russian Patients with Familial Hypercholesterolemia Using Targeted Next Generation Sequencing.

Dutch lipid clinic network criteria LDLR cardiovascular risk familial hypercholesterolemia next generation sequencing

Journal

Journal of cardiovascular development and disease
ISSN: 2308-3425
Titre abrégé: J Cardiovasc Dev Dis
Pays: Switzerland
ID NLM: 101651414

Informations de publication

Date de publication:
14 May 2020
Historique:
received: 27 02 2020
revised: 28 04 2020
accepted: 08 05 2020
entrez: 20 5 2020
pubmed: 20 5 2020
medline: 20 5 2020
Statut: epublish

Résumé

Russian patients with familial hypercholesterolemia (FH) were screened for pathogenic mutations using targeted next generation sequencing. Genetic testing was performed in 52 probands with definite or probable FH based on the Dutch lipid clinic network criteria (DLCN score ≥6). Blood samples were studied by massive parallel sequencing (Illumina HiSeq 1500 platform) using a custom capture library related to dyslipidemia and premature atherosclerosis. Mutations considered to be responsible for monogenic FH were identified in 48% of the probands: 24 with mutations in the

Identifiants

pubmed: 32423031
pii: jcdd7020016
doi: 10.3390/jcdd7020016
pmc: PMC7345545
pii:
doi:

Types de publication

Journal Article

Langues

eng

Déclaration de conflit d'intérêts

The authors declare no conflict of interest. The funders had no role in the design of the study; in the collection, analyses or interpretation of data; in the writing of the manuscript or in the decision to publish the results.

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Auteurs

Anna E Semenova (AE)

National Medical Research Center of Cardiology, 121552 Moscow, Russia.
Health in Code SL, Clinical Department, 15006 A Coruña, Spain.

Igor V Sergienko (IV)

National Medical Research Center of Cardiology, 121552 Moscow, Russia.

Diego García-Giustiniani (D)

Health in Code SL, Clinical Department, 15006 A Coruña, Spain.

Lorenzo Monserrat (L)

Health in Code SL, Clinical Department, 15006 A Coruña, Spain.

Anna B Popova (AB)

National Medical Research Center of Cardiology, 121552 Moscow, Russia.

Diana N Nozadze (DN)

National Medical Research Center of Cardiology, 121552 Moscow, Russia.

Marat V Ezhov (MV)

National Medical Research Center of Cardiology, 121552 Moscow, Russia.

Classifications MeSH