Severe diffuse alveolar hemorrhage related to autoimmune disease: a multicenter study.

ANCA-associated vasculitis Anti-MBG-associated vasculitis Antiphospholipid syndrome Cryoglobulinemia Diffuse alveolar hemorrhage ICU, mechanical ventilation IgA-associated vasculitis Plasma exchange Systemic lupus erythematosus

Journal

Critical care (London, England)
ISSN: 1466-609X
Titre abrégé: Crit Care
Pays: England
ID NLM: 9801902

Informations de publication

Date de publication:
18 05 2020
Historique:
received: 19 11 2019
accepted: 30 04 2020
entrez: 20 5 2020
pubmed: 20 5 2020
medline: 29 12 2020
Statut: epublish

Résumé

Diffuse alveolar hemorrhage (DAH) occurs during the course of autoimmune disease and may be life threatening. The objective was to assess characteristics and prognosis factors of DAH who required intensive care unit (ICU) admission in patients with autoimmune diseases. French multicenter retrospective study including patients presenting DAH related to autoimmune diseases requiring ICU admission from 2000 to 2016. One hundred four patients (54% of men) with median age of 56 [32-68] years were included with 79 (76%) systemic vasculitis and 25 (24%) connective tissue disorders. All patients received steroids, and 72 (69%), 12 (11.5%), and 57 (55%) patients had cyclophosphamide, rituximab, and plasma exchanges, respectively. During ICU stay, 52 (50%), 36 (35%), and 55 (53%) patients required mechanical ventilation, vasopressor use, and renal replacement therapy, respectively. Factors associated with mechanical ventilation weaning were age (HR [95%CI] 0.97 [0.96-0.99] per 10 years, p < 0.0001), vasculitis-related DAH (0.52 [0.27-0.98], p = 0.04), and time from dyspnea onset to ICU admission (0.99 [0.99-1] per day, p = 0.03). ICU mortality was 15%. Factors associated with alive status at ICU discharge were chronic cardiac failure (HR [95%CI] 0.37 [0.15-0.94], p = 0.04), antiphospholipid syndrome-related DAH (3.17 [1.89-5.32], p < 0.0001), SAPS II (0.98 [0.97-0.99], p = 0.007), and oxygen flow at ICU admission (0.95 [0.91-0.99] per liter/min, p = 0.04). DAH in autoimmune diseases is a life-threatening complication which requires mechanical ventilation in half of the cases admitted to ICU.

Sections du résumé

BACKGROUND
Diffuse alveolar hemorrhage (DAH) occurs during the course of autoimmune disease and may be life threatening. The objective was to assess characteristics and prognosis factors of DAH who required intensive care unit (ICU) admission in patients with autoimmune diseases.
METHODS
French multicenter retrospective study including patients presenting DAH related to autoimmune diseases requiring ICU admission from 2000 to 2016.
RESULTS
One hundred four patients (54% of men) with median age of 56 [32-68] years were included with 79 (76%) systemic vasculitis and 25 (24%) connective tissue disorders. All patients received steroids, and 72 (69%), 12 (11.5%), and 57 (55%) patients had cyclophosphamide, rituximab, and plasma exchanges, respectively. During ICU stay, 52 (50%), 36 (35%), and 55 (53%) patients required mechanical ventilation, vasopressor use, and renal replacement therapy, respectively. Factors associated with mechanical ventilation weaning were age (HR [95%CI] 0.97 [0.96-0.99] per 10 years, p < 0.0001), vasculitis-related DAH (0.52 [0.27-0.98], p = 0.04), and time from dyspnea onset to ICU admission (0.99 [0.99-1] per day, p = 0.03). ICU mortality was 15%. Factors associated with alive status at ICU discharge were chronic cardiac failure (HR [95%CI] 0.37 [0.15-0.94], p = 0.04), antiphospholipid syndrome-related DAH (3.17 [1.89-5.32], p < 0.0001), SAPS II (0.98 [0.97-0.99], p = 0.007), and oxygen flow at ICU admission (0.95 [0.91-0.99] per liter/min, p = 0.04).
CONCLUSION
DAH in autoimmune diseases is a life-threatening complication which requires mechanical ventilation in half of the cases admitted to ICU.

Identifiants

pubmed: 32423434
doi: 10.1186/s13054-020-02936-0
pii: 10.1186/s13054-020-02936-0
pmc: PMC7236262
doi:

Types de publication

Journal Article Multicenter Study

Langues

eng

Sous-ensembles de citation

IM

Pagination

231

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Auteurs

Adrien Mirouse (A)

Département Hospitalo-Universitaire Inflammation-Immunopathologie-Biotherapie (DHU i2B), UPMC Université Paris 06, UMR 7211, Sorbonne Universités, 75005, Paris, France.
INSERM, UMR_S 959, 75013, Paris, France.
CNRS, FRE3632, 75005, Paris, France.
Département de Médecine Interne et Immunologie Clinique, National Center for Autoimmune and Systemic Diseases and National Center for Autoinflammatory Diseases and Amyloidosis, APHP, Groupe Hospitalier Pitié-Salpêtrière, 75013, Paris, France.

Antoine Parrot (A)

Service de Pneumologie, Hôpital Tenon, APHP, Paris, France.

Vincent Audigier (V)

Département de Biostatistiques, Hôpital Saint-Louis, APHP, Paris, France.

Alexandre Demoule (A)

Service de Réanimation Médicale et Pneumologie, Hôpital Pitié-Salpêtrière, APHP, Paris, France.

Julien Mayaux (J)

Service de Réanimation Médicale et Pneumologie, Hôpital Pitié-Salpêtrière, APHP, Paris, France.

Guillaume Géri (G)

Service de Réanimation Médicale, Hôpital Cochin, APHP, Paris, France.

Eric Mariotte (E)

Service de Réanimation Médicale, Hôpital Saint-Louis, APHP, Paris, France.

Nicolas Bréchot (N)

Service de Réanimation Médicale, Hôpital Pitié-Salpêtrière, APHP, Paris, France.

Nicolas de Prost (N)

Service de Réanimation Médicale, Hôpital Henri Mondor, APHP, Créteil, France.

Mathieu Vautier (M)

Service de Médecine Interne, CHU de Caen, Caen, France.

Mathilde Neuville (M)

Service de Réanimation Médicale, Hôpital Bichat, APHP, Paris, France.

Naïke Bigé (N)

Service de Réanimation Médicale, Hôpital Saint-Antoine, Paris, France.

Etienne de Montmollin (E)

Service de Réanimation Medico-chirurgicale, Hôpital Delafontaine, Saint-Denis, France.

Patrice Cacoub (P)

Département Hospitalo-Universitaire Inflammation-Immunopathologie-Biotherapie (DHU i2B), UPMC Université Paris 06, UMR 7211, Sorbonne Universités, 75005, Paris, France.
INSERM, UMR_S 959, 75013, Paris, France.
CNRS, FRE3632, 75005, Paris, France.
Département de Médecine Interne et Immunologie Clinique, National Center for Autoimmune and Systemic Diseases and National Center for Autoinflammatory Diseases and Amyloidosis, APHP, Groupe Hospitalier Pitié-Salpêtrière, 75013, Paris, France.

Matthieu Resche-Rigon (M)

Département de Biostatistiques, Hôpital Saint-Louis, APHP, Paris, France.

Jacques Cadranel (J)

Service de Pneumologie, Hôpital Tenon, APHP, Paris, France.

David Saadoun (D)

Département Hospitalo-Universitaire Inflammation-Immunopathologie-Biotherapie (DHU i2B), UPMC Université Paris 06, UMR 7211, Sorbonne Universités, 75005, Paris, France. david.saadoun@aphp.fr.
INSERM, UMR_S 959, 75013, Paris, France. david.saadoun@aphp.fr.
CNRS, FRE3632, 75005, Paris, France. david.saadoun@aphp.fr.
Département de Médecine Interne et Immunologie Clinique, National Center for Autoimmune and Systemic Diseases and National Center for Autoinflammatory Diseases and Amyloidosis, APHP, Groupe Hospitalier Pitié-Salpêtrière, 75013, Paris, France. david.saadoun@aphp.fr.

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