Long-term outcomes of repaired and unrepaired truncus arteriosus: 20-year, single-center experience in Thailand.

Congenital heart defect Mortality risk Survival Truncus arteriosus

Journal

PeerJ
ISSN: 2167-8359
Titre abrégé: PeerJ
Pays: United States
ID NLM: 101603425

Informations de publication

Date de publication:
2020
Historique:
received: 16 09 2019
accepted: 17 04 2020
entrez: 22 5 2020
pubmed: 22 5 2020
medline: 22 5 2020
Statut: epublish

Résumé

Truncus arteriosus (TA) is a complex congenital heart disease that carries morbidities in the first year of life. Previous authors have reported an operative mortality of 50%. In this report, we aim to report on the survival of patients with TA in our medical center in the recent era. A retrospective review of all patients diagnosed with TA in Siriraj Hospital, Thailand from August 1995 to March 2018 was performed. Patients with single ventricle, hemiTA were excluded. The characteristics and outcomes of repaired and unrepaired TA patients with a known recent functional status in 2018 were reviewed. Operative mortality risks were analyzed using a multivariate model. A total of 74 patients (median age at referral: 70 days) were included in the cohort. One-third of the patients had associated anomalies including DiGeorge syndrome (13.5%). Anatomical repair was not performed in 22 patients (29.7%). The median age at time of repair for the 52 patients was 133 days (range: 22 days to 16.7 years). Complex TA was 10%. Early mortality occurred in 16 patients (30.8%). Five patients (9.6%) had late deaths at 0.3-1.2 years. Significant mortality risk was weight at time of operation <4 kg (HR 3.05, 95% CI [1.05-8.74], Contemporary survival rates of patients with TA following operation in the center has been gradually improved over time. Most of the operative mortality occurs in the early postoperative period. Compared to patients with TA who had palliative treatment, operative survivors have a better functional status even though they carry a risk for re-intervention.

Sections du résumé

BACKGROUND BACKGROUND
Truncus arteriosus (TA) is a complex congenital heart disease that carries morbidities in the first year of life. Previous authors have reported an operative mortality of 50%. In this report, we aim to report on the survival of patients with TA in our medical center in the recent era.
METHODS METHODS
A retrospective review of all patients diagnosed with TA in Siriraj Hospital, Thailand from August 1995 to March 2018 was performed. Patients with single ventricle, hemiTA were excluded. The characteristics and outcomes of repaired and unrepaired TA patients with a known recent functional status in 2018 were reviewed. Operative mortality risks were analyzed using a multivariate model.
RESULTS RESULTS
A total of 74 patients (median age at referral: 70 days) were included in the cohort. One-third of the patients had associated anomalies including DiGeorge syndrome (13.5%). Anatomical repair was not performed in 22 patients (29.7%). The median age at time of repair for the 52 patients was 133 days (range: 22 days to 16.7 years). Complex TA was 10%. Early mortality occurred in 16 patients (30.8%). Five patients (9.6%) had late deaths at 0.3-1.2 years. Significant mortality risk was weight at time of operation <4 kg (HR 3.05, 95% CI [1.05-8.74],
CONCLUSION CONCLUSIONS
Contemporary survival rates of patients with TA following operation in the center has been gradually improved over time. Most of the operative mortality occurs in the early postoperative period. Compared to patients with TA who had palliative treatment, operative survivors have a better functional status even though they carry a risk for re-intervention.

Identifiants

pubmed: 32435545
doi: 10.7717/peerj.9148
pii: 9148
pmc: PMC7227657
doi:

Types de publication

Journal Article

Langues

eng

Pagination

e9148

Informations de copyright

©2020 Dangrungroj et al.

Déclaration de conflit d'intérêts

The authors declare there are no competing interests.

Références

Can J Cardiol. 2019 Apr;35(4):446-452
pubmed: 30935635
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 1999;2:121-130
pubmed: 11486231
J Thorac Cardiovasc Surg. 1996 Apr;111(4):849-56
pubmed: 8614146
Ann Thorac Surg. 2013 Nov;96(5):1695-701; discussion 1701-2
pubmed: 23972424
J Thorac Cardiovasc Surg. 1993 Jun;105(6):1047-56
pubmed: 8501932
Ann Thorac Surg. 2012 Jan;93(1):164-9; discussion 169
pubmed: 22088417
Arch Surg. 1967 Nov;95(5):698-708
pubmed: 6053952
World J Pediatr Congenit Heart Surg. 2014 Apr;5(2):211-5
pubmed: 24668966
PLoS One. 2016 Jan 11;11(1):e0146800
pubmed: 26752522
Semin Thorac Cardiovasc Surg. 2016 Summer;28(2):500-511
pubmed: 28043468
Ann Thorac Surg. 2000 Apr;69(4 Suppl):S50-5
pubmed: 10798416
Congenit Heart Dis. 2016 Dec;11(6):672-677
pubmed: 27126954
Eur J Cardiothorac Surg. 2009 Oct;36(4):675-82
pubmed: 19464907
Circulation. 1976 Jul;54(1):108-11
pubmed: 1277412
Eur J Cardiothorac Surg. 1997 Apr;11(4):687-95; discussion 695-6
pubmed: 9151039
Eur J Cardiothorac Surg. 2001 Aug;20(2):221-7
pubmed: 11463535
Interact Cardiovasc Thorac Surg. 2019 Jul 1;29(1):93-100
pubmed: 30768164
Surg Clin North Am. 1949 Aug;29(4):1245-70
pubmed: 18141293
Eur J Cardiothorac Surg. 2008 May;33(5):890-8
pubmed: 18313324
World J Pediatr Congenit Heart Surg. 2015 Apr;6(2):226-38
pubmed: 25870342
Ann Thorac Surg. 1998 Dec;66(6 Suppl):S183-8
pubmed: 9930445
J Thorac Cardiovasc Surg. 1997 May;113(5):869-78; discussion 878-9
pubmed: 9159620
J Am Coll Cardiol. 1999 Aug;34(2):545-53
pubmed: 10440171
J Thorac Cardiovasc Surg. 2019 Jun;157(6):2386-2398.e4
pubmed: 30954295
J Am Coll Cardiol. 1999 Jul;34(1):223-32
pubmed: 10400015

Auteurs

Ekkachai Dangrungroj (E)

Department of Pediatrics, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Chodchanok Vijarnsorn (C)

Department of Pediatrics, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Prakul Chanthong (P)

Department of Pediatrics, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Paweena Chungsomprasong (P)

Department of Pediatrics, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Supaluck Kanjanauthai (S)

Department of Pediatrics, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Kritvikrom Durongpisitkul (K)

Department of Pediatrics, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Jarupim Soongswang (J)

Department of Pediatrics, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Kriangkrai Tantiwongkosri (K)

Department of Surgery, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Thaworn Subtaweesin (T)

Department of Surgery, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Somchai Sriyoschati (S)

Department of Surgery, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.

Classifications MeSH