MR imaging of cerebral involvement of Rosai-Dorfman disease: a single-centre experience with review of the literature.
MRI
RDD
Rosai–Dorfman disease
Spectroscopy
Journal
La Radiologia medica
ISSN: 1826-6983
Titre abrégé: Radiol Med
Pays: Italy
ID NLM: 0177625
Informations de publication
Date de publication:
Jan 2021
Jan 2021
Historique:
received:
03
11
2019
accepted:
12
05
2020
pubmed:
28
5
2020
medline:
23
2
2021
entrez:
28
5
2020
Statut:
ppublish
Résumé
Rosai-Dorfman disease (RDD) is a rare, benign, non-Langerhans cells histiocytosis with massive lymphadenopathy of uncertain aetiology. It is commonly characterized by massive, painless, non-tender, bilateral cervical lymphadenopathy. Extra-nodal involvement is usually seen in 50% of patients, with the brain being affected in only 5% of cases, usually as dural-based lesions. Clinical presentation is heterogeneous and strongly dependent on the localization of the lesions. Although the histopathological findings are essential for the final diagnosis, brain magnetic resonance imaging (MRI) currently represents the first-line strategy for the detection of the lesions across the central nervous system (CNS); moreover, it may provide additional elements for the differential diagnosis versus other more common lesions. We performed a case-based literature review to highlight possible aetiologic and pathogenetic theories of this disease, along with imaging features of RDD, with a particular focus on the MRI characteristics of the CNS involvement (CNS-RDD). Finally, we provided a novel insight on the current therapeutic approaches, either surgical or medical.
Identifiants
pubmed: 32458270
doi: 10.1007/s11547-020-01226-7
pii: 10.1007/s11547-020-01226-7
doi:
Substances chimiques
Contrast Media
0
iomeprol
17E17JBP8L
Iopamidol
JR13W81H44
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
89-98Commentaires et corrections
Type : ErratumIn
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