A Rare Cause of Refractory Chronic Diarrhea and Cachexia: A Case Report.

Neuroendocrine tumor Secretory diarrhea Somatostatin analogue Tunisia Vipoma

Journal

Iranian journal of public health
ISSN: 2251-6085
Titre abrégé: Iran J Public Health
Pays: Iran
ID NLM: 7505531

Informations de publication

Date de publication:
Feb 2020
Historique:
entrez: 29 5 2020
pubmed: 29 5 2020
medline: 29 5 2020
Statut: ppublish

Résumé

VIPoma is an unusual neuroendocrine neoplasm that autonomously secretes VIP. It is associated with secretory diarrhea and electrolyte disturbances. Herein we report a case of a male patient, who was hospitalized in the Department of Endocrinology in Hedi Chaker Hospital, Sfax, Tunisia. He presented VIPoma syndrome, with hepatic metastases at diagnosis. He had a history of chronic, watery diarrhea. He was dehydrated with many electrolytic disorders as hypokalemia, hyponatremia and metabolic acidosis. Abdominal CT scan showed a heterogeneous mass in the pancreatic head with multiple hepatic lesions. A high VIP hormone level was found. Histological study of a liver biopsy revealed hepatic metastases of neuroendocrine carcinoma. The patient received analogues of somatostatin and systemic chemotherapy, with a transient symptomatic relief. Sadly the patient was lost to follow-up.

Identifiants

pubmed: 32461947
pmc: PMC7231696

Types de publication

Case Reports

Langues

eng

Pagination

386-388

Informations de copyright

Copyright© Iranian Public Health Association & Tehran University of Medical Sciences.

Déclaration de conflit d'intérêts

Conflict of interests The authors declare that there is no conflict of interests.

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Auteurs

Faten Hadj Kacem (F)

Department of Endocrinology, Hedi Chaker Hospital, Sfax, Tunisia.

Donia Chebbi (D)

Department of Endocrinology, Hedi Chaker Hospital, Sfax, Tunisia.

Amal Chakroun (A)

Department of Endocrinology, Hedi Chaker Hospital, Sfax, Tunisia.

Nadia Charfi (N)

Department of Endocrinology, Hedi Chaker Hospital, Sfax, Tunisia.

Dorra Ghorbel (D)

Department of Endocrinology, Hedi Chaker Hospital, Sfax, Tunisia.

Fatma Mnif (F)

Department of Endocrinology, Hedi Chaker Hospital, Sfax, Tunisia.

Mouna Mnif (M)

Department of Endocrinology, Hedi Chaker Hospital, Sfax, Tunisia.

Nabila Rekik (N)

Department of Endocrinology, Hedi Chaker Hospital, Sfax, Tunisia.

Mohamed Abid (M)

Department of Endocrinology, Hedi Chaker Hospital, Sfax, Tunisia.

Classifications MeSH