Pumpless Lung Assist as a Bridge to Medical Therapy in a Teenager With Pulmonary Arterial Hypertension and Partial Anomalous Pulmonary Venous Return.


Journal

The Canadian journal of cardiology
ISSN: 1916-7075
Titre abrégé: Can J Cardiol
Pays: England
ID NLM: 8510280

Informations de publication

Date de publication:
11 2020
Historique:
received: 24 04 2020
revised: 27 05 2020
accepted: 01 06 2020
pubmed: 9 6 2020
medline: 20 5 2021
entrez: 9 6 2020
Statut: ppublish

Résumé

Heart failure is the main cause of death in patients with pulmonary arterial hypertension and congenital heart disease. We used an original approach in a 15-year-old girl with rapidly progressive right heart failure secondary to severe pulmonary arterial hypertension and partial anomalous pulmonary venous return. After surgical congenital heart defect repair on cardiopulmonary bypass, she was weaned off bypass using a central Novalung for 11 days, then started on triple specific pulmonary vasodilator therapy.

Identifiants

pubmed: 32512141
pii: S0828-282X(20)30519-5
doi: 10.1016/j.cjca.2020.06.001
pii:
doi:

Types de publication

Case Reports Research Support, Non-U.S. Gov't Video-Audio Media

Langues

eng

Sous-ensembles de citation

IM

Pagination

1831.e7-1831.e9

Informations de copyright

Copyright © 2020 Canadian Cardiovascular Society. Published by Elsevier Inc. All rights reserved.

Auteurs

Sébastien Hascoet (S)

Department of Congenital Heart Diseases, Centre Constitutif Malformations Cardiaques Congénitales Complexes M3C, Groupe Hospitalier Paris Saint-Joseph, Hôpital Marie Lannelongue, Plessis-Robinson, UMR-S 999, Inserm, Faculté de Médecine Paris-Saclay, Paris-Saclay University, France. Electronic address: s.hascoet@hml.fr.

Angèle Boet (A)

Department of Congenital Heart Diseases, Centre Constitutif Malformations Cardiaques Congénitales Complexes M3C, Groupe Hospitalier Paris Saint-Joseph, Hôpital Marie Lannelongue, Plessis-Robinson, UMR-S 999, Inserm, Faculté de Médecine Paris-Saclay, Paris-Saclay University, France.

Régine Roussin (R)

Department of Congenital Heart Diseases, Centre Constitutif Malformations Cardiaques Congénitales Complexes M3C, Groupe Hospitalier Paris Saint-Joseph, Hôpital Marie Lannelongue, Plessis-Robinson, UMR-S 999, Inserm, Faculté de Médecine Paris-Saclay, Paris-Saclay University, France.

Julien Guihaire (J)

Departments of Cardiac, Thoracic, and Vascular surgery, Centre de Référence de l'Hypertension Artérielle Pulmonaire Sévère, Groupe Hospitalier Paris Saint-Joseph, Hôpital Marie Lannelongue, Plessis-Robinson, Faculté de Médecine Paris-Saclay, Paris-Saclay University, France, UMR-S 999, Inserm, France.

Laurent Savale (L)

Department of Pneumology, Centre de Référence de l'Hypertension Pulmonaire Sévère, DHU Thorax Innovation, Hôpital Bicêtre, Le Kremlin-Bicêtre, France UMR-S 999, Inserm, Hôpital Marie Lannelongue, Faculté de Médecine Paris-Saclay, Université Paris-Saclay, France.

Olaf Mercier (O)

Departments of Cardiac, Thoracic, and Vascular surgery, Centre de Référence de l'Hypertension Artérielle Pulmonaire Sévère, Groupe Hospitalier Paris Saint-Joseph, Hôpital Marie Lannelongue, Plessis-Robinson, Faculté de Médecine Paris-Saclay, Paris-Saclay University, France, UMR-S 999, Inserm, France.

Elie Fadel (E)

Departments of Cardiac, Thoracic, and Vascular surgery, Centre de Référence de l'Hypertension Artérielle Pulmonaire Sévère, Groupe Hospitalier Paris Saint-Joseph, Hôpital Marie Lannelongue, Plessis-Robinson, Faculté de Médecine Paris-Saclay, Paris-Saclay University, France, UMR-S 999, Inserm, France.

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Classifications MeSH