A Case of Extensive Debilitating Generalized Morphea.

chronic pain immunosuppressants joint pain joint restriction methotrexate morphea rare skin disease restriction of motion scleroderma skin biopsy

Journal

Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737

Informations de publication

Date de publication:
14 May 2020
Historique:
entrez: 17 6 2020
pubmed: 17 6 2020
medline: 17 6 2020
Statut: epublish

Résumé

Morphea, also known as localized scleroderma, is an uncommon idiopathic inflammatory disorder leading to the development of sclerotic plaques in the skin. The disorder preferentially affects females. The pathogenesis of morphea is not well-understood. The disorder is likely to have an autoimmune basis; environmental and genetic factors may also play a role in its etiology. Morphea has a variety of clinical presentations. Lesions of morphea typically begin as inflammatory plaques or patches that evolve into firm sclerotic lesions. Involvement may be limited to the dermis or may extend to underlying subcutaneous fat, muscle, or bone. The identification of characteristic clinical findings is often sufficient for the diagnosis of morphea. A biopsy can be a useful tool when the diagnosis is in question or to obtain information on the depth and intensity of the disease, and it should always extend at least into the subcutaneous fat. Morphea may cause joint contractures and other impairments secondary to tissue sclerosis and can be very debilitating cosmetically and functionally.

Identifiants

pubmed: 32542170
doi: 10.7759/cureus.8117
pmc: PMC7292686
doi:

Types de publication

Case Reports

Langues

eng

Pagination

e8117

Informations de copyright

Copyright © 2020, Sapra et al.

Déclaration de conflit d'intérêts

The authors have declared that no competing interests exist.

Références

Front Med (Lausanne). 2017 Aug 18;4:120
pubmed: 28868289
Am J Clin Dermatol. 2017 Aug;18(4):491-512
pubmed: 28303481
J Am Acad Dermatol. 2017 Jun;76(6):1124-1130
pubmed: 28285783
Biomed Res Int. 2020 Mar 13;2020:9186274
pubmed: 32258158
Curr Rheumatol Rep. 2010 Feb;12(1):26-33
pubmed: 20425530
Pan Afr Med J. 2018 Jan 19;29:53
pubmed: 29875934
An Bras Dermatol. 2015 Jan-Feb;90(1):62-73
pubmed: 25672301
Open Dermatol J. 2009 Jan 1;3(1):22-31
pubmed: 21218179
Cochrane Database Syst Rev. 2019 Jul 16;7:CD005027
pubmed: 31309547
Presse Med. 2006 Dec;35(12 Pt 2):1923-8
pubmed: 17159718

Auteurs

Amit Sapra (A)

Family Medicine, Southern Illinois University School of Medicine, Springfield, USA.

Rebecca Dix (R)

Family Medicine, Southern Illinois University School of Medicine, Springfield, USA.

Priyanka Bhandari (P)

Family Medicine, Southern Illinois University School of Medicine, Springfield, USA.

Asiya Mohammed (A)

Family Medicine, Southern Illinois University School of Medicine, Springfield, USA.

Eukesh Ranjit (E)

Family Medicine, Southern Illinois University School of Medicine, Springfield, USA.

Classifications MeSH