Whole exome sequencing identifies compound heterozygous variants of

Respiratory medicine allergy/immunology paediatric primary immunodeficiencies whole exome sequencing

Journal

SAGE open medicine
ISSN: 2050-3121
Titre abrégé: SAGE Open Med
Pays: England
ID NLM: 101624744

Informations de publication

Date de publication:
2020
Historique:
received: 05 09 2019
accepted: 26 03 2020
entrez: 18 6 2020
pubmed: 18 6 2020
medline: 18 6 2020
Statut: epublish

Résumé

A pair of female Malay monozygotic twins who presented with recurrent upper respiratory tract infections, hepatosplenomegaly, bronchiectasis and bicytopenia were recruited in this study. Both patients were suspected with primary immunodeficiency diseases. However, the definite diagnosis was not clear due to complex disease phenotypes. The objective of this study was to identify the causative gene mutation in these patients. Lymphocyte subset enumeration test and whole exome sequencing were performed. We identified a compound heterozygous Whole exome sequencing analysis of the monozygotic twins revealed compound heterozygous missense mutations in

Identifiants

pubmed: 32547748
doi: 10.1177/2050312120922652
pii: 10.1177_2050312120922652
pmc: PMC7249565
doi:

Types de publication

Journal Article

Langues

eng

Pagination

2050312120922652

Informations de copyright

© The Author(s) 2020.

Déclaration de conflit d'intérêts

Declaration of conflicting interests: The author(s) declared no potential conflicts of interest with respect to the research, authorship, and/or publication of this article.

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Auteurs

Adiratna Mat Ripen (A)

Primary Immunodeficiency Unit, Allergy and Immunology Research Centre, Institute for Medical Research, Ministry of Health, Kuala Lumpur, Malaysia.

Hamidah Ghani (H)

Institute of Biological Sciences, Faculty of Science, University of Malaya, Kuala Lumpur, Malaysia.

Chai Teng Chear (CT)

Primary Immunodeficiency Unit, Allergy and Immunology Research Centre, Institute for Medical Research, Ministry of Health, Kuala Lumpur, Malaysia.

Mei Yee Chiow (MY)

Institute of Biological Sciences, Faculty of Science, University of Malaya, Kuala Lumpur, Malaysia.

Sharifah Nurul Husna Syed Yahya (SNH)

Primary Immunodeficiency Unit, Allergy and Immunology Research Centre, Institute for Medical Research, Ministry of Health, Kuala Lumpur, Malaysia.

Asiah Kassim (A)

Paediatric Institute, Kuala Lumpur Hospital, Ministry of Health, Kuala Lumpur, Malaysia.

Saharuddin Bin Mohamad (SB)

Institute of Biological Sciences, Faculty of Science, University of Malaya, Kuala Lumpur, Malaysia.
Centre of Research in Systems Biology, Structural Bioinformatics and Human Digital Imaging (CRYSTAL), University of Malaya, Kuala Lumpur, Malaysia.

Classifications MeSH