The ataxic neuropathies.
Ataxia
Dorsal ganglia
Immune-mediated
Neuronopathy
Paraneoplastic
Sensory
Sjögren
Journal
Journal of neurology
ISSN: 1432-1459
Titre abrégé: J Neurol
Pays: Germany
ID NLM: 0423161
Informations de publication
Date de publication:
Oct 2021
Oct 2021
Historique:
received:
23
04
2020
accepted:
10
06
2020
revised:
09
06
2020
pubmed:
20
6
2020
medline:
29
9
2021
entrez:
20
6
2020
Statut:
ppublish
Résumé
Ataxia is a frequent symptom in neurological cases with many causes. Sensory ataxia (due to involvement of the proprioceptive pathways) is observed in conditions affecting the central nervous system (spinal cord disorder) and the peripheral nervous system (peripheral neuropathy). The latter correspond to what we refer to as 'ataxic neuropathies'. Ataxic neuropathies represent a wide and heterogeneous spectrum of disorders that may affect dorsal root nerves, dorsal root ganglia, nerve trunks, distal nerve endings or all of them together. The identification of a predominant sensory ataxia in a case of peripheral neuropathy should raise the possibility of some specific etiologies. We propose here to present the main causes of ataxic neuropathies, which are identified with diagnostic workflows that are dictated by the topography of the likely sites of lesions in the proprioceptive pathway together with the timing of their occurrence (acute, subacute, or chronic).
Identifiants
pubmed: 32556571
doi: 10.1007/s00415-020-09994-y
pii: 10.1007/s00415-020-09994-y
doi:
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
3675-3689Informations de copyright
© 2020. Springer-Verlag GmbH Germany, part of Springer Nature.
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