Living donor liver transplantation for congenital absence of portal vein in portal venous reconstruction with a great saphenous vein graft.
Congenital absence of portal vein
Great saphenous vein transplantation
Living donor liver transplantation
Portal vein restructure
Journal
Surgical case reports
ISSN: 2198-7793
Titre abrégé: Surg Case Rep
Pays: Germany
ID NLM: 101662125
Informations de publication
Date de publication:
29 Jun 2020
29 Jun 2020
Historique:
received:
19
03
2020
accepted:
19
06
2020
entrez:
1
7
2020
pubmed:
1
7
2020
medline:
1
7
2020
Statut:
epublish
Résumé
Congenital absence of portal vein (CAPV) is a rare structural anomaly in which the portal vein (PV) blood that normally flow into the liver directly drains into the systemic venous system through other collateral circulation. Congenital portal vein shunts (CPSs) is classified into types I and II according to the absence or presence of the intrahepatic portal vein, respectively. The CPS type I is also known as CAPV. The liver transplantation may be the only treatment option for CAPV. The key point of liver transplantation for CAPV is the reconstruction of the PV. A 29-year-old man was diagnosed with CAPV with splenomegaly and gastroesophageal varix when being treated for pancytopenia and liver dysfunction. A living donor liver transplantation was performed for him using the right lobe which had been donated by his mother. The PV was reconstructed using his own great saphenous vein (GSV) as a graft vein. The end of the GSV graft was anastomosed to the inferior mesenteric vein while the other end was anastomosed to the vein graft of the right hepatic vein from the explanted liver. Using the patient's own GSV for PV reconstruction during living donor transplantation in the patient with CAPV seems to be an effective method.
Sections du résumé
BACKGROUND
BACKGROUND
Congenital absence of portal vein (CAPV) is a rare structural anomaly in which the portal vein (PV) blood that normally flow into the liver directly drains into the systemic venous system through other collateral circulation. Congenital portal vein shunts (CPSs) is classified into types I and II according to the absence or presence of the intrahepatic portal vein, respectively. The CPS type I is also known as CAPV. The liver transplantation may be the only treatment option for CAPV. The key point of liver transplantation for CAPV is the reconstruction of the PV.
CASE PRESENTATION
METHODS
A 29-year-old man was diagnosed with CAPV with splenomegaly and gastroesophageal varix when being treated for pancytopenia and liver dysfunction. A living donor liver transplantation was performed for him using the right lobe which had been donated by his mother. The PV was reconstructed using his own great saphenous vein (GSV) as a graft vein. The end of the GSV graft was anastomosed to the inferior mesenteric vein while the other end was anastomosed to the vein graft of the right hepatic vein from the explanted liver.
CONCLUSION
CONCLUSIONS
Using the patient's own GSV for PV reconstruction during living donor transplantation in the patient with CAPV seems to be an effective method.
Identifiants
pubmed: 32601822
doi: 10.1186/s40792-020-00916-8
pii: 10.1186/s40792-020-00916-8
pmc: PMC7324451
doi:
Types de publication
Journal Article
Langues
eng
Pagination
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