Rhabdoid Tumors Are Sensitive to the Protein-Translation Inhibitor Homoharringtonine.


Journal

Clinical cancer research : an official journal of the American Association for Cancer Research
ISSN: 1557-3265
Titre abrégé: Clin Cancer Res
Pays: United States
ID NLM: 9502500

Informations de publication

Date de publication:
15 09 2020
Historique:
received: 18 08 2019
revised: 30 05 2020
accepted: 29 06 2020
pubmed: 8 7 2020
medline: 15 12 2021
entrez: 8 7 2020
Statut: ppublish

Résumé

Rhabdoid tumors are devastating pediatric cancers in need of improved therapies. We sought to identify small molecules that exhibit We screened eight rhabdoid tumor cell lines with 481 small molecules and compared their sensitivity with that of 879 other cancer cell lines. Genome-scale CRISPR-Cas9 inactivation screens in rhabdoid tumors were analyzed to confirm target vulnerabilities. Gene expression and CRISPR-Cas9 data were queried across cell lines and primary rhabdoid tumors to discover biomarkers of small-molecule sensitivity. Molecular correlates were validated by manipulating gene expression. Subcutaneous rhabdoid tumor xenografts were treated with the most effective drug to confirm Small-molecule screening identified the protein-translation inhibitor homoharringtonine (HHT), an FDA-approved treatment for chronic myelogenous leukemia (CML), as the sole drug to which all rhabdoid tumor cell lines were selectively sensitive. Validation studies confirmed the sensitivity of rhabdoid tumor to HHT was comparable with that of CML cell lines. Low expression of the antiapoptotic gene Rhabdoid tumor cell lines and xenografts are highly sensitive to HHT, at least partially due to their low expression of

Identifiants

pubmed: 32631955
pii: 1078-0432.CCR-19-2717
doi: 10.1158/1078-0432.CCR-19-2717
pmc: PMC7501142
mid: NIHMS1609734
doi:

Substances chimiques

BCL2L1 protein, human 0
bcl-X Protein 0
Homoharringtonine 6FG8041S5B

Types de publication

Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

4995-5006

Subventions

Organisme : NIGMS NIH HHS
ID : T32 GM007226
Pays : United States
Organisme : NCI NIH HHS
ID : P50 CA101942
Pays : United States
Organisme : NCI NIH HHS
ID : R00 CA197640
Pays : United States
Organisme : NIGMS NIH HHS
ID : T32 GM007753
Pays : United States
Organisme : NCI NIH HHS
ID : R01 CA113794
Pays : United States
Organisme : NCI NIH HHS
ID : U01 CA176058
Pays : United States
Organisme : NCI NIH HHS
ID : R01 CA172152
Pays : United States

Informations de copyright

©2020 American Association for Cancer Research.

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Auteurs

Thomas P Howard (TP)

Department of Pediatric Oncology, Dana-Farber Cancer Institute and Division of Hematology/Oncology, Boston Children's Hospital, Boston, Massachusetts.
Department of Medical Oncology, Dana-Farber Cancer Institute, Boston, Massachusetts.
Broad Institute of Harvard and MIT, Cambridge, Massachusetts.
Harvard Medical School, Boston, Massachusetts.

Elaine M Oberlick (EM)

Department of Pediatric Oncology, Dana-Farber Cancer Institute and Division of Hematology/Oncology, Boston Children's Hospital, Boston, Massachusetts.
Broad Institute of Harvard and MIT, Cambridge, Massachusetts.

Matthew G Rees (MG)

Broad Institute of Harvard and MIT, Cambridge, Massachusetts.

Taylor E Arnoff (TE)

Department of Pediatric Oncology, Dana-Farber Cancer Institute and Division of Hematology/Oncology, Boston Children's Hospital, Boston, Massachusetts.
Department of Medical Oncology, Dana-Farber Cancer Institute, Boston, Massachusetts.

Minh-Tam Pham (MT)

Department of Pediatric Oncology, Dana-Farber Cancer Institute and Division of Hematology/Oncology, Boston Children's Hospital, Boston, Massachusetts.
Department of Medical Oncology, Dana-Farber Cancer Institute, Boston, Massachusetts.

Lisa Brenan (L)

Broad Institute of Harvard and MIT, Cambridge, Massachusetts.

Mariana DoCarmo (M)

Broad Institute of Harvard and MIT, Cambridge, Massachusetts.

Andrew L Hong (AL)

Department of Pediatric Oncology, Dana-Farber Cancer Institute and Division of Hematology/Oncology, Boston Children's Hospital, Boston, Massachusetts.
Department of Medical Oncology, Dana-Farber Cancer Institute, Boston, Massachusetts.
Broad Institute of Harvard and MIT, Cambridge, Massachusetts.
Department of Pediatrics, Emory University, Atlanta, Georgia.

Guillaume Kugener (G)

Broad Institute of Harvard and MIT, Cambridge, Massachusetts.

Hsien-Chao Chou (HC)

Comprehensive Cancer Center, St. Jude Children's Research Hospital, Memphis, Tennessee.
Department of Oncology, St. Jude Children's Research Hospital, Memphis, Tennessee.

Yiannis Drosos (Y)

Comprehensive Cancer Center, St. Jude Children's Research Hospital, Memphis, Tennessee.
Department of Oncology, St. Jude Children's Research Hospital, Memphis, Tennessee.

Kaeli M Mathias (KM)

Comprehensive Cancer Center, St. Jude Children's Research Hospital, Memphis, Tennessee.
Department of Oncology, St. Jude Children's Research Hospital, Memphis, Tennessee.

Pilar Ramos (P)

Comprehensive Cancer Center, St. Jude Children's Research Hospital, Memphis, Tennessee.
Department of Oncology, St. Jude Children's Research Hospital, Memphis, Tennessee.

Brinton Seashore-Ludlow (B)

Broad Institute of Harvard and MIT, Cambridge, Massachusetts.

Andrew O Giacomelli (AO)

Department of Medical Oncology, Dana-Farber Cancer Institute, Boston, Massachusetts.
Broad Institute of Harvard and MIT, Cambridge, Massachusetts.
Tumor Immunotherapy Program, Princess Margaret Cancer Centre, University Health Network, Toronto, Ontario, Canada.

Xiaofeng Wang (X)

Department of Pediatric Oncology, Dana-Farber Cancer Institute and Division of Hematology/Oncology, Boston Children's Hospital, Boston, Massachusetts.
Department of Molecular and Systems Biology, Geisel School of Medicine, Dartmouth College, Hanover, New Hampshire.

Burgess B Freeman (BB)

Preclinical Pharmacokinetics Shared Resource, St. Jude Children's Research Hospital, Memphis, Tennessee.

Kaley Blankenship (K)

Department of Oncology, St. Jude Children's Research Hospital, Memphis, Tennessee.

Lauren Hoffmann (L)

Department of Oncology, St. Jude Children's Research Hospital, Memphis, Tennessee.

Hong L Tiv (HL)

Experimental Therapeutics Core and Belfer Center for Applied Cancer Science, Dana-Farber Cancer Institute, Boston, Massachusetts.

Prafulla C Gokhale (PC)

Experimental Therapeutics Core and Belfer Center for Applied Cancer Science, Dana-Farber Cancer Institute, Boston, Massachusetts.

Cory M Johannessen (CM)

Broad Institute of Harvard and MIT, Cambridge, Massachusetts.

Elizabeth A Stewart (EA)

Comprehensive Cancer Center, St. Jude Children's Research Hospital, Memphis, Tennessee. charles.roberts@stjude.org elizabeth.stewart@stjude.org william_hahn@dfci.harvard.edu.
Department of Oncology, St. Jude Children's Research Hospital, Memphis, Tennessee.
Department of Developmental Neurobiology, St. Jude Children's Research Hospital, Memphis, Tennessee.

Stuart L Schreiber (SL)

Broad Institute of Harvard and MIT, Cambridge, Massachusetts.
Department of Chemistry and Chemical Biology, Harvard University, Cambridge, Massachusetts.

William C Hahn (WC)

Department of Medical Oncology, Dana-Farber Cancer Institute, Boston, Massachusetts. charles.roberts@stjude.org elizabeth.stewart@stjude.org william_hahn@dfci.harvard.edu.
Broad Institute of Harvard and MIT, Cambridge, Massachusetts.
Harvard Medical School, Boston, Massachusetts.

Charles W M Roberts (CWM)

Department of Pediatric Oncology, Dana-Farber Cancer Institute and Division of Hematology/Oncology, Boston Children's Hospital, Boston, Massachusetts. charles.roberts@stjude.org elizabeth.stewart@stjude.org william_hahn@dfci.harvard.edu.
Broad Institute of Harvard and MIT, Cambridge, Massachusetts.
Harvard Medical School, Boston, Massachusetts.
Comprehensive Cancer Center, St. Jude Children's Research Hospital, Memphis, Tennessee.
Department of Oncology, St. Jude Children's Research Hospital, Memphis, Tennessee.

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