Epithelial vectorial ion transport in cystic fibrosis: Dysfunction, measurement, and pharmacotherapy to target the primary deficit.
Respiratory medicine
ion transport
pharmacoeconomics/health economics
Journal
SAGE open medicine
ISSN: 2050-3121
Titre abrégé: SAGE Open Med
Pays: England
ID NLM: 101624744
Informations de publication
Date de publication:
2020
2020
Historique:
received:
11
02
2019
accepted:
21
05
2020
entrez:
9
7
2020
pubmed:
9
7
2020
medline:
9
7
2020
Statut:
epublish
Résumé
Cystic fibrosis patients display multi-organ system dysfunction (e.g. pancreas, gastrointestinal tract, and lung) with pathogenesis linked to a failure of Cl
Identifiants
pubmed: 32637102
doi: 10.1177/2050312120933807
pii: 10.1177_2050312120933807
pmc: PMC7323271
doi:
Types de publication
Journal Article
Review
Langues
eng
Pagination
2050312120933807Commentaires et corrections
Type : ErratumIn
Informations de copyright
© The Author(s) 2020.
Déclaration de conflit d'intérêts
Declaration of conflicting interests: The author(s) declared the following potential conflicts of interest with respect to the research, authorship, and/or publication of this article: The authors whose names are listed certify that they have no affiliations with or involvement in any organization or entity with any financial interest (such as honoraria; educational grants; participation in speakers’ bureaus; membership, employment, consultancies, stock ownership, or other equity interest; and expert testimony or patent-licensing arrangements), or non-financial interest (such as personal or professional relationships, affiliations, knowledge, or beliefs) in the subject matter or materials discussed in this article.
Références
Am J Respir Crit Care Med. 2013 Jun 1;187(11):1219-25
pubmed: 23590265
J Cyst Fibros. 2014 Mar;13(2):139-47
pubmed: 24660233
Diabetes Care. 2009 Sep;32(9):1626-31
pubmed: 19542209
Science. 1995 Aug 11;269(5225):847-50
pubmed: 7543698
Lancet Respir Med. 2016 Feb;4(2):107-15
pubmed: 26803277
J Biol Chem. 2010 Nov 12;285(46):35825-35
pubmed: 20667826
J Biol Chem. 1997 May 30;272(22):14037-40
pubmed: 9162024
Am J Respir Crit Care Med. 2018 Jun 1;197(11):1433-1442
pubmed: 29327948
J Clin Invest. 1996 Sep 15;98(6):1304-12
pubmed: 8823295
Lancet Respir Med. 2014 Jul;2(7):527-38
pubmed: 24973281
N Engl J Med. 2018 Oct 25;379(17):1612-1620
pubmed: 30334692
N Engl J Med. 2015 Jul 16;373(3):220-31
pubmed: 25981758
Lancet Respir Med. 2014 Nov;2(11):902-910
pubmed: 25311995
Am J Physiol. 1997 Sep;273(3 Pt 1):C988-98
pubmed: 9316420
Lancet Respir Med. 2018 Jul;6(7):545-553
pubmed: 29886024
J Cyst Fibros. 2015 Mar;14(2):169-77
pubmed: 25677689
Lancet Respir Med. 2015 Jul;3(7):524-33
pubmed: 26070913
J Cyst Fibros. 2019 Jan;18(1):22-34
pubmed: 29934203
Am J Respir Cell Mol Biol. 2016 Mar;54(3):312-8
pubmed: 26562629
Lancet Respir Med. 2017 Jul;5(7):557-567
pubmed: 28606620
Mol Biol Cell. 2005 May;16(5):2154-67
pubmed: 15716351
Lancet Respir Med. 2017 Feb;5(2):107-118
pubmed: 28011037
Nature. 1992 Aug 27;358(6389):761-4
pubmed: 1380673
J Hepatol. 2004 Dec;41(6):920-5
pubmed: 15582124
J Heart Lung Transplant. 2005 Oct;24(10):1522-9
pubmed: 16210125
N Engl J Med. 2005 Oct 6;353(14):1443-53
pubmed: 16207846
Mol Biol Cell. 2016 Feb 1;27(3):424-33
pubmed: 26823392
Lancet. 2019 Nov 23;394(10212):1940-1948
pubmed: 31679946
Nat Rev Genet. 2015 Jan;16(1):45-56
pubmed: 25404111
J Clin Invest. 1984 Jun;73(6):1763-71
pubmed: 6327771
N Engl J Med. 2011 Nov 3;365(18):1663-72
pubmed: 22047557
Ann Am Thorac Soc. 2017 Feb;14(2):213-219
pubmed: 27898234
Sci Transl Med. 2014 Jul 23;6(246):246ra96
pubmed: 25101886
J Pediatr Gastroenterol Nutr. 2005 Feb;40(2):199-201
pubmed: 15699697
N Engl J Med. 2018 Oct 25;379(17):1599-1611
pubmed: 30334693
Front Pharmacol. 2013 Apr 23;4:40
pubmed: 23630497
J Biol Chem. 2005 Feb 18;280(7):5221-6
pubmed: 15582996
J Cyst Fibros. 2014 Dec;13(6):674-80
pubmed: 25266159
Drugs R D. 2016 Mar;16(1):1-17
pubmed: 26747453
PLoS One. 2013 Dec 06;8(12):e81545
pubmed: 24324701
Lancet Respir Med. 2016 Aug;4(8):617-626
pubmed: 27298017
Pediatr Pulmonol. 2014 Feb;49(2):106-17
pubmed: 24249707
Curr Opin Pharmacol. 2008 Jun;8(3):292-9
pubmed: 18468487
Ann Am Thorac Soc. 2017 Nov;14(11):1662-1666
pubmed: 28406713
Am J Respir Crit Care Med. 2015 Oct 1;192(7):836-42
pubmed: 26132840
N Engl J Med. 2017 Nov 23;377(21):2024-2035
pubmed: 29099333
Am J Respir Crit Care Med. 2017 Apr 1;195(7):912-920
pubmed: 27805836
Cell Mol Life Sci. 2017 Jan;74(1):93-115
pubmed: 27714410
Genet Med. 2014 Jul;16(7):539-46
pubmed: 24357848
Pediatrics. 2007 Dec;120(6):1311-6
pubmed: 18055681
J Pediatr Gastroenterol Nutr. 1990 Oct;11(3):356-60
pubmed: 2246718
Lancet Respir Med. 2013 Oct;1(8):630-638
pubmed: 24461666
J Cyst Fibros. 2011 May;10(3):187-92
pubmed: 21354377
Nat Med. 2004 May;10(5):487-93
pubmed: 15077107
Am J Respir Crit Care Med. 2018 Jan 15;197(2):214-224
pubmed: 28930490
Nature. 1990 Sep 27;347(6291):358-63
pubmed: 1699126
Hum Gene Ther. 1995 Apr;6(4):445-55
pubmed: 7542031
Physiology (Bethesda). 2007 Jun;22:212-25
pubmed: 17557942
J Cyst Fibros. 2016 Jan;15(1):116-22
pubmed: 25682022
J Pediatr. 2017 Feb;181S:S4-S15.e1
pubmed: 28129811
Am J Respir Crit Care Med. 2005 Mar 15;171(6):621-6
pubmed: 15591474
Chest. 2012 Sep;142(3):718-724
pubmed: 22383668
N Engl J Med. 2019 Nov 7;381(19):1809-1819
pubmed: 31697873