The morbid cutaneous anatomy of the human genome revealed by a bioinformatic approach.


Journal

Genomics
ISSN: 1089-8646
Titre abrégé: Genomics
Pays: United States
ID NLM: 8800135

Informations de publication

Date de publication:
11 2020
Historique:
received: 13 09 2019
revised: 28 03 2020
accepted: 02 07 2020
pubmed: 11 7 2020
medline: 16 9 2021
entrez: 11 7 2020
Statut: ppublish

Résumé

Computational approaches have been developed to prioritize candidate genes in disease gene identification. They are based on different pieces of evidences associating each gene with the given disease. In this study, 648 genes underlying genodermatoses have been compared to 1808 genes involved in other genetic diseases using a bioinformatic approach. These genes were studied at the structural, evolutionary and functional levels. Results show that genes underlying genodermatoses present longer CDS and have more exons. Significant differences were observed in nucleotide motif and amino-acid compositions. Evolutionary conservation analysis revealed that genodermatoses genes have less paralogs, more orthologs in Mouse and Dog and are less conserved. Functional analysis revealed that genodermatosis genes seem to be involved in immune system and skin layers. The Bayesian network model returned a rate of good classification of around 80%. This computational approach could help investigators working in the field of dermatology by prioritizing positional candidate genes for mutation screening.

Identifiants

pubmed: 32650097
pii: S0888-7543(19)30663-9
doi: 10.1016/j.ygeno.2020.07.009
pii:
doi:

Substances chimiques

Proteins 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

4232-4241

Informations de copyright

Copyright © 2020 Elsevier Inc. All rights reserved.

Auteurs

Lilia Romdhane (L)

Biomedical Genomics and Oncogenetics Laboratory LR11IPT05, LR16IPT05, Institut Pasteur de Tunis, Université Tunis El Manar, Tunis, Tunisia; Department of Biology, Faculty of Sciences of Bizerte, Jarzouna, Université Tunis Carthage, Tunis, Tunisia. Electronic address: lilia.romdhane@fsb.rnu.tn.

Heni Bouhamed (H)

Molecular and Cellular Screening Process Laboratory, Centre of Biotechnology of Sfax, Sfax, Tunisia.

Kais Ghedira (K)

Laboratory of Bioinformatics, Biomathematics and Biostatistics (LR16IPT09), Institut Pasteur de Tunis, Université Tunis El Manar, Tunis, Tunisia.

Cherif Ben Hamda (C)

Laboratory of Bioinformatics, Biomathematics and Biostatistics (LR16IPT09), Institut Pasteur de Tunis, Université Tunis El Manar, Tunis, Tunisia.

Amel Louhichi (A)

Molecular and Cellular Screening Process Laboratory, Centre of Biotechnology of Sfax, Sfax, Tunisia.

Haifa Jmel (H)

Biomedical Genomics and Oncogenetics Laboratory LR11IPT05, LR16IPT05, Institut Pasteur de Tunis, Université Tunis El Manar, Tunis, Tunisia.

Safa Romdhane (S)

Biomedical Genomics and Oncogenetics Laboratory LR11IPT05, LR16IPT05, Institut Pasteur de Tunis, Université Tunis El Manar, Tunis, Tunisia.

Chérine Charfeddine (C)

Biomedical Genomics and Oncogenetics Laboratory LR11IPT05, LR16IPT05, Institut Pasteur de Tunis, Université Tunis El Manar, Tunis, Tunisia; High Institut of Biotechnology of Sidi Thabet, University of Manouba, BiotechPole of Sidi Thabet, Ariana, Tunisia.

Mourad Mokni (M)

Department of Dermatology, CHU La Rabta Tunis, Tunis, Tunisia; Public health and infection Research Laboratory, La Rabta Hospital, Tunis, Tunisia.

Sonia Abdelhak (S)

Biomedical Genomics and Oncogenetics Laboratory LR11IPT05, LR16IPT05, Institut Pasteur de Tunis, Université Tunis El Manar, Tunis, Tunisia.

Ahmed Rebai (A)

Molecular and Cellular Screening Process Laboratory, Centre of Biotechnology of Sfax, Sfax, Tunisia.

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