Case of melorheostosis associated with ipsilateral verrucous epidermal nevus, linear connective tissue nevus, diffuse hyperpigmentation and hypertrichosis: A fortuitous coincidence?
connective tissue nevus
hyperpigmentation
hypertrichosis
melorheostosis
verrucous epidermal nevus
Journal
The Journal of dermatology
ISSN: 1346-8138
Titre abrégé: J Dermatol
Pays: England
ID NLM: 7600545
Informations de publication
Date de publication:
Sep 2020
Sep 2020
Historique:
received:
29
08
2019
accepted:
11
05
2020
pubmed:
14
7
2020
medline:
15
5
2021
entrez:
14
7
2020
Statut:
ppublish
Résumé
Melorheostosis (MEL) is a rare benign bone disorder that can be associated with several anomalies, including vascular abnormalities, nevus sebaceus, unilateral nevoid telangiectasia, linear scleroderma and hypertrichosis. We report the case of a 6-year-old patient who showed an unusual co-occurrence of bone hyperostosis and different skin lesions affecting the same side of the body: MEL, verrucous epidermal nevus, connective tissue nevus, linear scleroderma-like disorder, hyperpigmentation and hypertrichosis. The spatial co-occurrence of these conditions made us speculate as to whether they originated from a common genetic mechanism or if their co-occurrence was completely accidental.
Identifiants
pubmed: 32656852
doi: 10.1111/1346-8138.15460
doi:
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
1063-1066Informations de copyright
© 2020 Japanese Dermatological Association.
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