Periaortitis and diffuse subendocardial vasculitis in a patient with systemic lupus erythematosus - Lupus flare or a coexisting disease?

Systemic lupus erythematosus antiphospholipid syndrome diffuse subendocardial vasculitis periaortitis

Journal

Mediterranean journal of rheumatology
ISSN: 2529-198X
Titre abrégé: Mediterr J Rheumatol
Pays: Greece
ID NLM: 101730166

Informations de publication

Date de publication:
Jun 2020
Historique:
received: 31 10 2019
revised: 25 11 2019
accepted: 28 11 2019
entrez: 18 7 2020
pubmed: 18 7 2020
medline: 18 7 2020
Statut: epublish

Résumé

Systemic lupus erythematosus (SLE) is a heterogeneous disease with a broad spectrum of clinical manifestations. Periaortitis is a rare disorder which may manifest isolated or in association with other autoimmune diseases, including SLE. Another rare, yet severe cardiovascular manifestation of lupus is diffuse subendocardial vasculitis (DSV), which should be suspected in patients presenting with myocardial hypokinesis, impaired ejection fraction and normal coronary angiography. Cardiovascular Magnetic Resonance (CMR) imaging is crucial to distinguish between DSV and lupus myocarditis, which should also be included in the differential diagnosis. Herein, we describe a case of a female patient with pre-existing SLE, who presented with both periaortitis and DSV, and discuss the diagnostic challenges associated with these rare manifestations.

Identifiants

pubmed: 32676560
doi: 10.31138/mjr.31.2.216
pii: mjr-31-2-216
pmc: PMC7362120
doi:

Types de publication

Case Reports

Langues

eng

Pagination

216-219

Informations de copyright

© 2020 The Mediterranean Journal of Rheumatology (MJR).

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Auteurs

Ourania Gioti (O)

Department of Rheumatology, Asklepieion General Hospital, Athens, Greece.

Evangelos Theotikos (E)

Department of Rheumatology, Asklepieion General Hospital, Athens, Greece.

Argyro Lazarini (A)

Department of Rheumatology, Asklepieion General Hospital, Athens, Greece.

Andreas S Triantafyllis (AS)

Department of Cardiology, Asklepieion General Hospital, Athens, Greece.

Alexia Balanika (A)

Department of Radiology, Asklepieion General Hospital, Athens, Greece.

Maria Boutsikou (M)

Cardiac MRI Unit, Mediterraneo Hospital, Athens, Greece.

Pavlos Tsinivizov (P)

Department of Cardiology, Asklepieion General Hospital, Athens, Greece.

Antonis Fanouriakis (A)

Department of Rheumatology, Asklepieion General Hospital, Athens, Greece.

Antonia Elezoglou (A)

Department of Rheumatology, Asklepieion General Hospital, Athens, Greece.

Classifications MeSH