Fibrodysplasia ossificans progressiva with two emergency laparotomies: A case report.
Case report
Fibrodysplasia ossificans progressiva
General surgery
Heterotopic ossification
Journal
International journal of surgery case reports
ISSN: 2210-2612
Titre abrégé: Int J Surg Case Rep
Pays: Netherlands
ID NLM: 101529872
Informations de publication
Date de publication:
2020
2020
Historique:
received:
22
04
2020
revised:
28
06
2020
accepted:
03
07
2020
pubmed:
22
7
2020
medline:
22
7
2020
entrez:
22
7
2020
Statut:
ppublish
Résumé
Fibrodysplasia ossificans progressiva (FOP) is a disorder causing progressive heterotopic ossification of muscles, tendons, and ligaments. Invasive procedures such as surgery should be avoided, because physical stimulation causes heterotopic ossification. A 40-year-old Japanese man with FOP was transported to our hospital with sudden abdominal pain. Emergency surgery was performed because a computed tomography scan showed the presence of intraabdominal free air. We diagnosed peritonitis due to perforation of Meckel's diverticulum and performed a small intestinal resection. The day after surgery, airway obstruction was recognized, and tracheostomy was required. Six months after surgery, a strangulated small bowel obstruction developed, and a second laparotomy was performed. As the patient continued to have difficulty swallowing, we constructed a gastrostomy at the time of the second surgery. He was discharged with no complications. Ossification of the abdominal incision wound due to surgical invasion was suspected, but it did not occur in the short term. Two laparotomies could be performed safely in a patient with FOP.
Identifiants
pubmed: 32693234
pii: S2210-2612(20)30544-7
doi: 10.1016/j.ijscr.2020.07.033
pmc: PMC7384327
pii:
doi:
Types de publication
Case Reports
Langues
eng
Pagination
196-198Informations de copyright
Copyright © 2020 The Author(s). Published by Elsevier Ltd.. All rights reserved.
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