Bulbospinal muscular atrophy (Kennedy disease) responsive to immunoglobulins?

Kennedy disease immunoglobulins motor neuron disease phenotype polyglutamine disease polyneuropathy

Journal

Clinical case reports
ISSN: 2050-0904
Titre abrégé: Clin Case Rep
Pays: England
ID NLM: 101620385

Informations de publication

Date de publication:
Jul 2020
Historique:
received: 23 11 2019
revised: 30 03 2020
accepted: 02 04 2020
entrez: 23 7 2020
pubmed: 23 7 2020
medline: 23 7 2020
Statut: epublish

Résumé

A 61 year old man with facial diplegia, quadruparesis, tongue atrophy/fasciculations, bulbar speech, muscle weakness/wasting, hypotonia, tremor, dysdiadochokinesia, absent tendon reflexes, fasciculations, and gynecomastia, received immunoglobulins for suspected immune-neuropathy with limited benefit. After reconsideration, Kennedy disease was diagnosed upon 44 CAG repeats in

Identifiants

pubmed: 32695362
doi: 10.1002/ccr3.2899
pii: CCR32899
pmc: PMC7364100
doi:

Types de publication

Case Reports

Langues

eng

Pagination

1223-1225

Informations de copyright

© 2020 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd.

Déclaration de conflit d'intérêts

There are no conflicts of interest.

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Auteurs

Katharina Poustka (K)

Department of Neurology Kaiser Franz Josef Spital Vienna Austria.

Sabine Pollanz-Petrovic (S)

Department of Neurology Kaiser Franz Josef Spital Vienna Austria.

Elisabeth Lindeck-Pozza (E)

Department of Neurology Kaiser Franz Josef Spital Vienna Austria.

Josef Finsterer (J)

Krankenanstalt Rudolfstiftung Messerli Institute Vienna Austria.

Classifications MeSH