Bone marrow fibrosis, sequence variant of asxl1, and Sjögren syndrome: A case report.

ASXL1 Sjögren syndrome autoimmune bone marrow fibrosis molecular

Journal

Clinical case reports
ISSN: 2050-0904
Titre abrégé: Clin Case Rep
Pays: England
ID NLM: 101620385

Informations de publication

Date de publication:
Jul 2020
Historique:
received: 25 09 2019
revised: 18 02 2020
accepted: 29 02 2020
entrez: 23 7 2020
pubmed: 23 7 2020
medline: 23 7 2020
Statut: epublish

Résumé

Only proven pathogenic mutations associated with myeloid neoplasms are key to establish the clonal nature of the bone marrow fibrosis. In cases with genetic variants of uncertain meaning, the clinical picture may be required to rule out secondary causes.

Identifiants

pubmed: 32695373
doi: 10.1002/ccr3.2813
pii: CCR32813
pmc: PMC7364095
doi:

Types de publication

Case Reports

Langues

eng

Pagination

1269-1273

Informations de copyright

© 2020 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd.

Déclaration de conflit d'intérêts

None declared.

Références

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Auteurs

Marta Santaliestra (M)

Hematology Department Hospital de la Santa Creu i Sant Pau Universitat Autònoma de Barcelona Barcelona Spain.

Elena Bussaglia (E)

Hematology Department Hospital de la Santa Creu i Sant Pau Universitat Autònoma de Barcelona Barcelona Spain.

Marta Pratcorona (M)

Hematology Department Hospital de la Santa Creu i Sant Pau Universitat Autònoma de Barcelona Barcelona Spain.

Anna Monter-Rovira (A)

Hematology Department Hospital de la Santa Creu i Sant Pau Universitat Autònoma de Barcelona Barcelona Spain.

Silvana Saavedra (S)

Hematology Department Hospital de la Santa Creu i Sant Pau Universitat Autònoma de Barcelona Barcelona Spain.

Anna Mozos (A)

Pathology Department Hospital de la Santa Creu i Sant Pau Universitat Autònoma de Barcelona Barcelona Spain.

Clara Martínez (C)

Hematology Department Hospital de la Santa Creu i Sant Pau Universitat Autònoma de Barcelona Barcelona Spain.

Josep F Nomdedéu (JF)

Hematology Department Hospital de la Santa Creu i Sant Pau Universitat Autònoma de Barcelona Barcelona Spain.

Classifications MeSH