Life-Threatening Intraventricular Rupture of Brain Abscess in a Patient With Undiagnosed Hereditary Hemorrhagic Telangiectasia.
arteriovenous malformation
brain abscess
hereditary hemorrhagic telangiectasia
intraventricular rupture of brain abscess
osler-weber-rendu
pulmonary arteriovenous malformation
septic emboli
ventriculitis
Journal
Cureus
ISSN: 2168-8184
Titre abrégé: Cureus
Pays: United States
ID NLM: 101596737
Informations de publication
Date de publication:
21 Jun 2020
21 Jun 2020
Historique:
entrez:
28
7
2020
pubmed:
28
7
2020
medline:
28
7
2020
Statut:
epublish
Résumé
Hereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant genetic condition associated with mucocutaneous and visceral arteriovenous malformations (AVMs), including pulmonary AVMs, which predispose patients to systemic paradoxical emboli that can lead to brain abscesses. Intraventricular rupture of brain abscess (IVROBA) is a feared complication with a high mortality rate. Here, we present a case with brain abscesses complicated by IVROBA and ventriculitis as the initial presentation of HHT in an undiagnosed patient. We also discuss the diagnostic and therapeutic approach that resulted in this patient's clinical improvement.
Identifiants
pubmed: 32714672
doi: 10.7759/cureus.8732
pmc: PMC7377030
doi:
Types de publication
Case Reports
Langues
eng
Pagination
e8732Informations de copyright
Copyright © 2020, Nguyen et al.
Déclaration de conflit d'intérêts
The authors have declared that no competing interests exist.
Références
Neurosurgery. 2001 Feb;48(2):310-6; discussion 316-7
pubmed: 11220373
Cardiovasc Diagn Ther. 2018 Jun;8(3):325-337
pubmed: 30057879
QJM. 2002 Aug;95(8):501-9
pubmed: 12145389
J Clin Neurosci. 2020 Jan;71:191-198
pubmed: 31439482
Otolaryngol Clin North Am. 2018 Feb;51(1):237-254
pubmed: 29217066
Eur J Clin Microbiol Infect Dis. 2017 Oct;36(10):1975-1980
pubmed: 28578477
Neurology. 2000 Oct 10;55(7):959-64
pubmed: 11061251
Surg Neurol. 2006 Jun;65(6):557-62; discussion 562
pubmed: 16720170
Nat Rev Immunol. 2017 Jan;17(1):7-20
pubmed: 27890913
Clin Neurol Neurosurg. 2012 Apr;114(3):235-40
pubmed: 22093524
Eur Radiol. 2018 Mar;28(3):1338-1344
pubmed: 29018941
Am J Med Genet. 2000 Mar 6;91(1):66-7
pubmed: 10751092
Am J Respir Crit Care Med. 1998 Aug;158(2):643-61
pubmed: 9700146
Haematologica. 2019 Feb;104(2):e85-e86
pubmed: 30705116