Clinical and Functional Characteristics of Patients with Unclassifiable Interstitial Lung Disease (uILD): Long-Term Follow-Up Data from European IPF Registry (eurIPFreg).
European Registry for idiopathic pulmonary fibrosis (eurIPFreg)
Health-related quality of life (HRQoL)
idiopathic pulmonary fibrosis (IPF)
interstitial lung diseases (ILD)
unclassifiable interstitial lung disease (uILD)
Journal
Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588
Informations de publication
Date de publication:
03 Aug 2020
03 Aug 2020
Historique:
received:
07
07
2020
revised:
26
07
2020
accepted:
31
07
2020
entrez:
7
8
2020
pubmed:
7
8
2020
medline:
7
8
2020
Statut:
epublish
Résumé
(1) Aim of the study: In spite of extensive research, up to 20% of interstitial lung diseases (ILD) patients cannot be safely classified. We analyzed clinical features, progression factors, and outcomes of unclassifiable ILD (uILD). (2) Methods: A total of 140 uILD subjects from the University of Giessen and Marburg Lung Center (UGMLC) were recruited between 11/2009 and 01/2019 into the European Registry for idiopathic pulmonary fibrosis (eurIPFreg) and followed until 01/2020. The diagnosis of uILD was applied only when a conclusive diagnosis could not be reached with certainty. (3) Results: In 46.4% of the patients, the uILD diagnosis was due to conflicting clinical, radiological, and pathological data. By applying the diagnostic criteria of usual interstitial pneumonia (UIP) based on computed tomography (CT), published by the Fleischner Society, 22.2% of the patients displayed a typical UIP pattern. We also showed that forced vital capacity (FVC) at baseline (
Identifiants
pubmed: 32756496
pii: jcm9082499
doi: 10.3390/jcm9082499
pmc: PMC7464480
pii:
doi:
Types de publication
Journal Article
Langues
eng
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