3p25 microdeletion syndrome KBG syndrome MRD23 SETD5 haploinsufficiency WES

Journal

Frontiers in neurology
ISSN: 1664-2295
Titre abrégé: Front Neurol
Pays: Switzerland
ID NLM: 101546899

Informations de publication

Date de publication:
2020
Historique:
received: 03 04 2020
accepted: 28 05 2020
entrez: 15 8 2020
pubmed: 15 8 2020
medline: 15 8 2020
Statut: epublish

Résumé

Mendelian disorders of the epigenetic machinery (MDEMs), also named chromatin modifying disorders, are a broad group of neurodevelopmental disorders, caused by mutations in functionally related chromatin genes. Mental retardation autosomal dominant 23 (MRD23) syndrome, due to

Identifiants

pubmed: 32793091
doi: 10.3389/fneur.2020.00631
pmc: PMC7393934
doi:

Types de publication

Journal Article

Langues

eng

Pagination

631

Informations de copyright

Copyright © 2020 Crippa, Bestetti, Maitz, Weiss, Spano, Masciadri, Smithson, Larizza, Low, Cohen and Finelli.

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Auteurs

Milena Crippa (M)

Research Laboratory of Medical Cytogenetics and Molecular Genetics, IRCCS Istituto Auxologico Italiano, Milan, Italy.
Department of Medical Biotechnology and Translational Medicine, University of Milan, Milan, Italy.

Ilaria Bestetti (I)

Research Laboratory of Medical Cytogenetics and Molecular Genetics, IRCCS Istituto Auxologico Italiano, Milan, Italy.
Department of Medical Biotechnology and Translational Medicine, University of Milan, Milan, Italy.

Silvia Maitz (S)

Clinical Pediatric Genetic Unit, Pediatric Clinic, Fondazione MBBM, San Gerardo Hospital, Monza, Italy.

Karin Weiss (K)

The Genetics Institute, Rambam Health Care Campus, Haifa, Israel.

Alice Spano (A)

Clinical Pediatric Genetic Unit, Pediatric Clinic, Fondazione MBBM, San Gerardo Hospital, Monza, Italy.

Maura Masciadri (M)

Medical Cytogenetics and Molecular Genetics Laboratory, IRCCS Istituto Auxologico Italiano, Milan, Italy.

Sarah Smithson (S)

Clinical Genetics, St. Michael's Hospital, University Hospitals NHS Trust, Bristol, United Kingdom.

Lidia Larizza (L)

Research Laboratory of Medical Cytogenetics and Molecular Genetics, IRCCS Istituto Auxologico Italiano, Milan, Italy.

Karen Low (K)

Clinical Genetics, St. Michael's Hospital, University Hospitals NHS Trust, Bristol, United Kingdom.

Lior Cohen (L)

Genetics Unit, Barzilai University Medical Center, Ashkelon, Israel.
Faculty of Health Sciences, Ben-Gurion University of the Negev, Be'er Sheva, Israel.

Palma Finelli (P)

Research Laboratory of Medical Cytogenetics and Molecular Genetics, IRCCS Istituto Auxologico Italiano, Milan, Italy.
Department of Medical Biotechnology and Translational Medicine, University of Milan, Milan, Italy.

Classifications MeSH