Portal cavernoma or chronic non cirrhotic extrahepatic portal vein obstruction.
Cavernoma cholangiopathy
Portal cavernoma
Variceal
Journal
Clinics and research in hepatology and gastroenterology
ISSN: 2210-741X
Titre abrégé: Clin Res Hepatol Gastroenterol
Pays: France
ID NLM: 101553659
Informations de publication
Date de publication:
09 2020
09 2020
Historique:
received:
26
02
2020
accepted:
03
03
2020
pubmed:
21
8
2020
medline:
21
10
2021
entrez:
22
8
2020
Statut:
ppublish
Résumé
Chronic non cirrhotic extrahepatic portal vein obstruction (EHPVO) refers to the cavernomatous transformation of the portal vein (the so-called "portal cavernoma") which occurs following acute thrombosis of the portal vein in the absence of recanalization. In adults, EHPVO mainly occurs following thrombosis, while in children it may be related to congenital malformations and/or neonatal umbilical venous catheterization. However, 50% of the cases of EHPVO remain idiopathic [1]. Risk factors and associated diseases should be investigated (chapter 1). Indeed, the presence of a thrombophilic alteration, in particular myeloproliferative neoplasm impacts prognosis and determine a causal treatment.
Identifiants
pubmed: 32819872
pii: S2210-7401(20)30091-7
doi: 10.1016/j.clinre.2020.03.016
pii:
doi:
Types de publication
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
491-496Informations de copyright
Copyright © 2020 Elsevier Masson SAS. All rights reserved.