Expression Patterns of Coagulation Factor XIII Subunit A on Leukemic Lymphoblasts Correlate with Clinical Outcome and Genetic Subtypes in Childhood B-cell Progenitor Acute Lymphoblastic Leukemia.

B-cell progenitor Factor XIII subunit A acute lymphoblastic leukemia children genetic risk categories middle-income countries survival

Journal

Cancers
ISSN: 2072-6694
Titre abrégé: Cancers (Basel)
Pays: Switzerland
ID NLM: 101526829

Informations de publication

Date de publication:
13 Aug 2020
Historique:
received: 20 06 2020
revised: 03 08 2020
accepted: 10 08 2020
entrez: 23 8 2020
pubmed: 23 8 2020
medline: 23 8 2020
Statut: epublish

Résumé

Based on previous retrospective results, we investigated the association of coagulation FXIII subunit A (FXIII-A) expression pattern on survival and correlations with known prognostic factors of B-cell progenitor (BCP) childhood acute lymphoblastic leukemia (ALL) as a pilot study of the prospective multi-center BFM ALL-IC 2009 clinical trial. The study included four national centers ( Three different patterns of FXIII-A expression were observed: negative (<20%), dim (20-79%), and bright (≥80%). The FXIII-A dim expression group had significantly higher 5-year event-free survival (EFS) (93%) than the FXIII-A negative (70%) and FXIII-A bright (61%) groups. Distribution of intermediate genetic risk categories and the "B-other" genetic subgroup differed significantly between the FXIII-A positive and negative groups. Multivariate logistic regression confirmed independent association between the FXIII-A negative expression characteristics and the prevalence of intermediate genetic risk group. FXIII-A negativity is associated with dismal survival in children with BCP-ALL and is an indicator for the presence of unfavorable genetic alterations.

Sections du résumé

BACKGROUND BACKGROUND
Based on previous retrospective results, we investigated the association of coagulation FXIII subunit A (FXIII-A) expression pattern on survival and correlations with known prognostic factors of B-cell progenitor (BCP) childhood acute lymphoblastic leukemia (ALL) as a pilot study of the prospective multi-center BFM ALL-IC 2009 clinical trial.
METHODS METHODS
The study included four national centers (
RESULTS RESULTS
Three different patterns of FXIII-A expression were observed: negative (<20%), dim (20-79%), and bright (≥80%). The FXIII-A dim expression group had significantly higher 5-year event-free survival (EFS) (93%) than the FXIII-A negative (70%) and FXIII-A bright (61%) groups. Distribution of intermediate genetic risk categories and the "B-other" genetic subgroup differed significantly between the FXIII-A positive and negative groups. Multivariate logistic regression confirmed independent association between the FXIII-A negative expression characteristics and the prevalence of intermediate genetic risk group.
CONCLUSIONS CONCLUSIONS
FXIII-A negativity is associated with dismal survival in children with BCP-ALL and is an indicator for the presence of unfavorable genetic alterations.

Identifiants

pubmed: 32823516
pii: cancers12082264
doi: 10.3390/cancers12082264
pmc: PMC7463512
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : Hungarian Science Foundation
ID : K108885
Organisme : Polish National Center for Research and Development
ID : STRATEGMED3/304586/5/NVBR/2017

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Auteurs

Bettina Kárai (B)

Department of Laboratory of Medicine, University of Debrecen, 4032 Debrecen, Hungary.

Katalin Gyurina (K)

Department of Pediatrics, University of Debrecen, 4032 Debrecen, Hungary.

Anikó Ujfalusi (A)

Department of Laboratory of Medicine, University of Debrecen, 4032 Debrecen, Hungary.

Łukasz Sędek (Ł)

Department of Microbiology and Immunology, Medical University of Silesia, 40-055 Katowice, Poland.

Gábor Barna (G)

1st Department of Pathology and Experimental Cancer Research, Semmelweis University, 1085 Budapest, Hungary.

Pál Jáksó (P)

Department of Pathology, Scientific University of Pécs, 7622 Pécs, Hungary.

Peter Svec (P)

Department of Pediatric Hematology and Oncology, National Institute of Children's Diseases and Comenius University Bratislava, 833 40 Bratislava, Slovakia.

Eszter Szánthó (E)

Department of Laboratory of Medicine, University of Debrecen, 4032 Debrecen, Hungary.

Attila Csaba Nagy (AC)

Department of Preventive Medicine, Faculty of Public Health, University of Debrecen, 4028 Debrecen, Hungary.

Judit Müller (J)

2nd Department of Pediatrics, Semmelweis University, 1094 Budapest, Hungary.

Réka Simon (R)

Department of Pediatric Hematology-Oncology, BAZ county university hospital pediatric center, 3526 Miskolc, Hungary.

Ágnes Vojczek (Á)

Department of Pediatrics, Scientific University of Pécs, 7622 Pécs, Hungary.

István Szegedi (I)

Department of Pediatrics, University of Debrecen, 4032 Debrecen, Hungary.

Lilla Györgyi Tiszlavicz (LG)

Department of Pediatrics, Scientific University of Szeged, 6720 Szeged, Hungary.

Jerzy R Kowalczyk (JR)

Department of Pediatric Hematology, Oncology and Transplantology, Lublin Medical University, 20-059 Lublin, Poland.

Alexandra Kolenova (A)

Department of Pediatric Hematology and Oncology, National Institute of Children's Diseases and Comenius University Bratislava, 833 40 Bratislava, Slovakia.

Gábor T Kovács (GT)

2nd Department of Pediatrics, Semmelweis University, 1094 Budapest, Hungary.

Tomasz Szczepański (T)

Department of Pediatric Hematology and Oncology, Medical University of Silesia Zabrze, 41-808 Zabrze, Poland.

Michael Dworzak (M)

Children's Cancer Research Institute and St. Anna Children's Hospital, Pediatric Clinic, Medical University of Vienna, 1090 Vienna, Austria.

Angela Schumich (A)

Children's Cancer Research Institute and St. Anna Children's Hospital, Pediatric Clinic, Medical University of Vienna, 1090 Vienna, Austria.

Andishe Attarbaschi (A)

Children's Cancer Research Institute and St. Anna Children's Hospital, Pediatric Clinic, Medical University of Vienna, 1090 Vienna, Austria.

Karin Nebral (K)

Children's Cancer Research Institute and St. Anna Children's Hospital, Pediatric Clinic, Medical University of Vienna, 1090 Vienna, Austria.

Oskar A Haas (OA)

Children's Cancer Research Institute and St. Anna Children's Hospital, Pediatric Clinic, Medical University of Vienna, 1090 Vienna, Austria.

János Kappelmayer (J)

Department of Laboratory of Medicine, University of Debrecen, 4032 Debrecen, Hungary.

Zsuzsanna Hevessy (Z)

Department of Laboratory of Medicine, University of Debrecen, 4032 Debrecen, Hungary.

Csongor Kiss (C)

Department of Pediatrics, University of Debrecen, 4032 Debrecen, Hungary.

Classifications MeSH