Altered Sensory Neuron Development in CMT2D Mice Is Site-Specific and Linked to Increased GlyRS Levels.

Charcot-Marie-Tooth disease (CMT) aminoacyl-tRNA synthetase (ARS) amyotrophic lateral sclerosis (ALS) axonal transport glycyl-tRNA synthetase (GlyRS) neurotrophin receptors (Trks) sensory neuron signaling endosome

Journal

Frontiers in cellular neuroscience
ISSN: 1662-5102
Titre abrégé: Front Cell Neurosci
Pays: Switzerland
ID NLM: 101477935

Informations de publication

Date de publication:
2020
Historique:
received: 27 04 2020
accepted: 01 07 2020
entrez: 28 8 2020
pubmed: 28 8 2020
medline: 28 8 2020
Statut: epublish

Résumé

Dominant, missense mutations in the widely and constitutively expressed

Identifiants

pubmed: 32848623
doi: 10.3389/fncel.2020.00232
pmc: PMC7431706
doi:

Types de publication

Journal Article

Langues

eng

Pagination

232

Subventions

Organisme : Medical Research Council
ID : MR/S006990/1
Pays : United Kingdom

Informations de copyright

Copyright © 2020 Sleigh, Mech, Aktar, Zhang and Schiavo.

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Auteurs

James N Sleigh (JN)

Department of Neuromuscular Diseases, UCL Queen Square Institute of Neurology, University College London, London, United Kingdom.
UK Dementia Research Institute, University College London, London, United Kingdom.

Aleksandra M Mech (AM)

Department of Neuromuscular Diseases, UCL Queen Square Institute of Neurology, University College London, London, United Kingdom.

Tahmina Aktar (T)

Department of Neuromuscular Diseases, UCL Queen Square Institute of Neurology, University College London, London, United Kingdom.

Yuxin Zhang (Y)

Department of Neuromuscular Diseases, UCL Queen Square Institute of Neurology, University College London, London, United Kingdom.

Giampietro Schiavo (G)

Department of Neuromuscular Diseases, UCL Queen Square Institute of Neurology, University College London, London, United Kingdom.
UK Dementia Research Institute, University College London, London, United Kingdom.
Discoveries Centre for Regenerative and Precision Medicine, University College London Campus, London, United Kingdom.

Classifications MeSH