Isolated blast crisis relapse in the central nervous system of a patient treating for a chronic myelogenous leukemia.


Journal

The Pan African medical journal
ISSN: 1937-8688
Titre abrégé: Pan Afr Med J
Pays: Uganda
ID NLM: 101517926

Informations de publication

Date de publication:
2020
Historique:
received: 08 06 2020
accepted: 19 06 2020
entrez: 3 9 2020
pubmed: 3 9 2020
medline: 23 12 2020
Statut: epublish

Résumé

Chronic myeloid leukemia (CML) is a myeloproliferative disorder associated with the Philadelphia chromosome t (9;22) and the BCR-ABL fusion gene. The condition is relatively rare, accounting for 2.0% to 3.0% of childhood leukemia cases. CML has historically been a triphasic disease. Most patients are diagnosed in chronic phase. Without treatment, it inevitably progresses into a more aggressive accelerated phase and blast crisis. Some proportion of CML cases of blastic transformation develop an extramedullary disease that involves rarely central nervous system. This report describe an extremely rare case of 13-year-old girl with CML and extramedullary blast crisis in the central nervous system. Treatment options and monitoring of disease response are discussed.

Identifiants

pubmed: 32874406
doi: 10.11604/pamj.2020.36.142.24155
pii: PAMJ-36-142
pmc: PMC7436633
doi:

Substances chimiques

Imatinib Mesylate 8A1O1M485B

Types de publication

Case Reports Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

142

Informations de copyright

Copyright: Houda Boudiaf et al.

Déclaration de conflit d'intérêts

The authors declare no competing interests.

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Auteurs

Houda Boudiaf (H)

Department of Pediatric Oncology, University Hospital of Mustapha Pacha, Algiers, Algeria.

Khedaoudj Ezziane (K)

Department of Pediatric Oncology, University Hospital of Mustapha Pacha, Algiers, Algeria.

Nassiba Ould Rouis (NO)

Department of Pediatric Oncology, University Hospital of Mustapha Pacha, Algiers, Algeria.

Meriem Himrane (M)

Department of Pediatric Oncology, University Hospital of Mustapha Pacha, Algiers, Algeria.

Saliha Hakem (S)

Department of Pediatric Oncology, University Hospital of Mustapha Pacha, Algiers, Algeria.

Hanifa Benchabane (H)

Department of Pediatric Oncology, University Hospital of Mustapha Pacha, Algiers, Algeria.

Houria Boukhelal (H)

Department of Pediatric Oncology, University Hospital of Mustapha Pacha, Algiers, Algeria.

Radja Arous (R)

Department of Pediatric Oncology, University Hospital of Mustapha Pacha, Algiers, Algeria.

Lynda Chikhi (L)

Department of Blood Transfusion and Hemobiology, University Hospital of Mustapha Pacha, Algiers, Algeria.

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