Altered DNA methylation profiles in blood from patients with sporadic Creutzfeldt-Jakob disease.


Journal

Acta neuropathologica
ISSN: 1432-0533
Titre abrégé: Acta Neuropathol
Pays: Germany
ID NLM: 0412041

Informations de publication

Date de publication:
12 2020
Historique:
received: 10 07 2020
accepted: 31 08 2020
revised: 13 08 2020
pubmed: 13 9 2020
medline: 22 9 2021
entrez: 12 9 2020
Statut: ppublish

Résumé

Prion diseases are fatal and transmissible neurodegenerative disorders caused by the misfolding and aggregation of prion protein. Although recent studies have implicated epigenetic variation in common neurodegenerative disorders, no study has yet explored their role in human prion diseases. Here we profiled genome-wide blood DNA methylation in the most common human prion disease, sporadic Creutzfeldt-Jakob disease (sCJD). Our case-control study (n = 219), when accounting for differences in cell type composition between individuals, identified 38 probes at genome-wide significance (p < 1.24 × 10

Identifiants

pubmed: 32918118
doi: 10.1007/s00401-020-02224-9
pii: 10.1007/s00401-020-02224-9
pmc: PMC7666287
doi:

Substances chimiques

Shaker Superfamily of Potassium Channels 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

863-879

Subventions

Organisme : Medical Research Council
ID : MC_U123160657
Pays : United Kingdom
Organisme : Medical Research Council
ID : MC_U123160651
Pays : United Kingdom
Organisme : Medical Research Council
ID : MC_UU_00024/1
Pays : United Kingdom
Organisme : Medical Research Council
ID : MC_UU_00024/9
Pays : United Kingdom
Organisme : Medical Research Council
ID : G0400713
Pays : United Kingdom

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Auteurs

Luke C Dabin (LC)

MRC Prion Unit at UCL, UCL Institute of Prion Diseases, Courtauld Building, 33 Cleveland Street, London, W1W 7FF, UK.

Fernando Guntoro (F)

MRC Prion Unit at UCL, UCL Institute of Prion Diseases, Courtauld Building, 33 Cleveland Street, London, W1W 7FF, UK.

Tracy Campbell (T)

MRC Prion Unit at UCL, UCL Institute of Prion Diseases, Courtauld Building, 33 Cleveland Street, London, W1W 7FF, UK.

Tony Bélicard (T)

MRC London Institute of Medical Sciences Du Cane Road London W12 0NN and Institute of Clinical Sciences, Imperial College London Du Cane Road London W12 0NN, Imperial College London, London, W12 0NN, UK.

Adam R Smith (AR)

College of Medicine and Health, University of Exeter Medical School, Exeter University, RILD Building Level 4, Royal Devon and Exeter Hospital, Barrack Rd, Exeter, EX2 5DW, UK.

Rebecca G Smith (RG)

College of Medicine and Health, University of Exeter Medical School, Exeter University, RILD Building Level 4, Royal Devon and Exeter Hospital, Barrack Rd, Exeter, EX2 5DW, UK.

Rachel Raybould (R)

Institute of Psychological Medicine and Clinical Neurosciences, Cardiff University, UHW Main Building, Heath Park, Cardiff, CF14 4XN, UK.

Jonathan M Schott (JM)

Dementia Research Centre, UCL Institute of Neurology, 8-11 Queen Square, London, WC1N 3AR, UK.

Katie Lunnon (K)

College of Medicine and Health, University of Exeter Medical School, Exeter University, RILD Building Level 4, Royal Devon and Exeter Hospital, Barrack Rd, Exeter, EX2 5DW, UK.

Peter Sarkies (P)

MRC London Institute of Medical Sciences Du Cane Road London W12 0NN and Institute of Clinical Sciences, Imperial College London Du Cane Road London W12 0NN, Imperial College London, London, W12 0NN, UK.

John Collinge (J)

MRC Prion Unit at UCL, UCL Institute of Prion Diseases, Courtauld Building, 33 Cleveland Street, London, W1W 7FF, UK.

Simon Mead (S)

MRC Prion Unit at UCL, UCL Institute of Prion Diseases, Courtauld Building, 33 Cleveland Street, London, W1W 7FF, UK. s.mead@prion.ucl.ac.uk.

Emmanuelle Viré (E)

MRC Prion Unit at UCL, UCL Institute of Prion Diseases, Courtauld Building, 33 Cleveland Street, London, W1W 7FF, UK.

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Classifications MeSH