Japanese patients with mitochondrial 3-hydroxy-3-methylglutaryl-CoA synthase deficiency:

C2/C0 bacterial expression system disease-causing mutation functional analysis mitochondrial 3-hydroxy-3-methylglutaryl-CoA synthase

Journal

Experimental and therapeutic medicine
ISSN: 1792-0981
Titre abrégé: Exp Ther Med
Pays: Greece
ID NLM: 101531947

Informations de publication

Date de publication:
Nov 2020
Historique:
received: 11 12 2019
accepted: 17 06 2020
entrez: 21 9 2020
pubmed: 22 9 2020
medline: 22 9 2020
Statut: ppublish

Résumé

Mitochondrial 3-hydroxy-3-methylglutaryl-CoA synthase (HMGCS2) deficiency is a metabolic disorder caused by mutations in the

Identifiants

pubmed: 32952630
doi: 10.3892/etm.2020.9166
pii: ETM-0-0-09166
pmc: PMC7480138
doi:

Banques de données

figshare
['10.6084/m9.figshare.10308536.v1']

Types de publication

Journal Article

Langues

eng

Pagination

39

Informations de copyright

Copyright: © Ago et al.

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Auteurs

Yasuhiko Ago (Y)

Department of Pediatrics, Graduate School of Medicine, Gifu University Hospital, Gifu, Gifu 501-1194, Japan.

Hiroki Otsuka (H)

Department of Pediatrics, Graduate School of Medicine, Gifu University Hospital, Gifu, Gifu 501-1194, Japan.

Hideo Sasai (H)

Department of Pediatrics, Graduate School of Medicine, Gifu University Hospital, Gifu, Gifu 501-1194, Japan.
Clinical Genetics Center, Gifu University Hospital, Gifu, Gifu 501-1194, Japan.

Elsayed Abdelkreem (E)

Department of Pediatrics, Faculty of Medicine, Sohag University, Sohag 82524, Egypt.

Mina Nakama (M)

Department of Pediatrics, Graduate School of Medicine, Gifu University Hospital, Gifu, Gifu 501-1194, Japan.
Clinical Genetics Center, Gifu University Hospital, Gifu, Gifu 501-1194, Japan.

Yuka Aoyama (Y)

Department of Biomedical Sciences, College of Life and Health Sciences, Education and Training Center of Medical Technology, Chubu University, Kasugai, Aichi 487-8501, Japan.

Hideki Matsumoto (H)

Department of Pediatrics, Graduate School of Medicine, Gifu University Hospital, Gifu, Gifu 501-1194, Japan.

Ryoji Fujiki (R)

Department of Applied Genomics, Kazusa DNA Research Institute, Kisarazu, Chiba 292-0818, Japan.

Osamu Ohara (O)

Department of Applied Genomics, Kazusa DNA Research Institute, Kisarazu, Chiba 292-0818, Japan.

Kazumasa Akiyama (K)

Akiyama Children's Clinic, Kitami, Hokkaido 090-0051, Japan.

Kaori Fukui (K)

Department of Pediatrics and Child Health, Kurume University School of Medicine, Kurume, Fukuoka 830-0011, Japan.

Yoriko Watanabe (Y)

Department of Pediatrics and Child Health, Kurume University School of Medicine, Kurume, Fukuoka 830-0011, Japan.
Research Institute of Medical Mass Spectrometry, Kurume University School of Medicine, Kurume, Fukuoka 830-0011, Japan.

Yoko Nakajima (Y)

Department of Pediatrics, Fujita Health University School of Medicine, Toyoake, Aichi 470-1192, Japan.

Hidenori Ohnishi (H)

Department of Pediatrics, Graduate School of Medicine, Gifu University Hospital, Gifu, Gifu 501-1194, Japan.

Tetsuya Ito (T)

Department of Pediatrics, Fujita Health University School of Medicine, Toyoake, Aichi 470-1192, Japan.

Toshiyuki Fukao (T)

Department of Pediatrics, Graduate School of Medicine, Gifu University Hospital, Gifu, Gifu 501-1194, Japan.
Clinical Genetics Center, Gifu University Hospital, Gifu, Gifu 501-1194, Japan.

Classifications MeSH