Extraskeletal Myxoid Chondrosarcoma: State of the Art and Current Research on Biology and Clinical Management.

NR4A3 fusions antiangiogenics chemotherapy chondrosarcoma sarcoma

Journal

Cancers
ISSN: 2072-6694
Titre abrégé: Cancers (Basel)
Pays: Switzerland
ID NLM: 101526829

Informations de publication

Date de publication:
21 Sep 2020
Historique:
received: 28 07 2020
revised: 11 09 2020
accepted: 17 09 2020
entrez: 24 9 2020
pubmed: 25 9 2020
medline: 25 9 2020
Statut: epublish

Résumé

Extraskeletal myxoid chondrosarcoma (EMC) is an ultra-rare mesenchymal neoplasm with uncertain differentiation, which arises mostly in the deep soft tissue of proximal extremities and limb girdles. EMC is marked by a translocation involving the

Identifiants

pubmed: 32967265
pii: cancers12092703
doi: 10.3390/cancers12092703
pmc: PMC7563993
pii:
doi:

Types de publication

Journal Article Review

Langues

eng

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Auteurs

Silvia Stacchiotti (S)

Medical Oncology Unit 2, Cancer Medicine Department, Fondazione IRCCS Istituto Nazionale Tumori, 20133 Milan, Italy.

Giacomo Giulio Baldi (GG)

"Sandro Pitigliani" Medical Oncology Department, Hospital of Prato, 59100 Prato, Italy.

Carlo Morosi (C)

Deparment of Radiology, Fondazione IRCCS Istituto Nazionale Tumori, 20133 Milan, Italy.

Alessandro Gronchi (A)

Department of Surgery, Fondazione IRCCS Istituto Nazionale Tumori, 20133 Milan, Italy.

Roberta Maestro (R)

Unit of Oncogenetics and Functional Oncogenomics, Centro di Riferimento Oncologico di Aviano (CRO) IRCCS, National Cancer Institute, 33081 Aviano, Italy.

Classifications MeSH