Patients with both Langerhans cell histiocytosis and Crohn's disease highlight a common role of interleukin-23.


Journal

Acta paediatrica (Oslo, Norway : 1992)
ISSN: 1651-2227
Titre abrégé: Acta Paediatr
Pays: Norway
ID NLM: 9205968

Informations de publication

Date de publication:
04 2021
Historique:
received: 12 08 2020
revised: 16 09 2020
accepted: 17 09 2020
pubmed: 26 9 2020
medline: 15 5 2021
entrez: 25 9 2020
Statut: ppublish

Résumé

To present the first case series of patients with Langerhans cell histiocytosis (LCH) also affected by Crohn's disease (CD), both of which are granulomatous diseases, and in LCH investigate the role of interleukin (IL)-23, which is a well-described disease mediator in CD. A case series of three patients with LCH and CD were described; a cohort of LCH patients (n = 55) as well as controls (n = 55) were analysed for circulating IL-23 levels; and the relation between the percentage of LCH cells in lesions and circulating IL-23 levels was analysed in seven LCH patients. Differential diagnostic challenges for these two granulomatous diseases were highlighted in the case series, and it took up to 3 years to diagnose CD. Elevated IL-23 levels were found in LCH patients. The amount of lesional LCH cells correlated with the levels of circulating IL-23. Both CD and LCH should be considered in patients with inflammatory gastrointestinal involvement. The IL-23 pathway is a common immunological trait between these two granulomatous diseases.

Identifiants

pubmed: 32975844
doi: 10.1111/apa.15590
pmc: PMC7984331
doi:

Substances chimiques

Interleukin-23 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

1315-1321

Informations de copyright

©2020 The Authors. Acta Paediatrica published by John Wiley & Sons Ltd on behalf of Foundation Acta Paediatrica.

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Auteurs

Egle Kvedaraite (E)

Childhood Cancer Research Unit, Department of Women's and Children's Health, Karolinska Institutet, Stockholm, Sweden.
Center for Infectious Medicine, Department of Medicine Huddinge, Karolinska Institutet, Stockholm, Sweden.

Magda Lourda (M)

Childhood Cancer Research Unit, Department of Women's and Children's Health, Karolinska Institutet, Stockholm, Sweden.
Center for Infectious Medicine, Department of Medicine Huddinge, Karolinska Institutet, Stockholm, Sweden.

HongYa Han (H)

Center for Hematology and Regenerative Medicine, Department of Medicine Huddinge, Karolinska Institutet, Stockholm, Sweden.

Bianca Tesi (B)

Centre for Molecular Medicine, Department of Molecular Medicine and Surgery, Karolinska Institutet, Stockholm, Sweden.
Department of Clinical Genetics, Karolinska University Laboratory, Karolinska University Hospital, Stockholm, Sweden.

Jenée Mitchell (J)

Fiona Elsey Cancer Research Institute and Federation University Australia, Ballarat, Vic., Australia.

Maja Ideström (M)

Department of Pediatric Gastroenterology, Hepatology and Nutrition, Karolinska University Hospital, Stockholm, Sweden.

Natalia Mouratidou (N)

Department of Pediatric Gastroenterology, Hepatology and Nutrition, Karolinska University Hospital, Stockholm, Sweden.

George Rassidakis (G)

Department of Oncology-Pathology, Karolinska University Hospital, Stockholm, Sweden.

Tatiana von Bahr Greenwood (T)

Childhood Cancer Research Unit, Department of Women's and Children's Health, Karolinska Institutet, Stockholm, Sweden.
Department of Pediatric Oncology, Karolinska University Hospital, Stockholm, Sweden.

Fleur Cohen-Aubart (F)

Institut E3M, Centre National de Référence des Histiocytoses, Hôpital Pitié-Salpêtrière, Sorbonne Université, Paris, France.

Martin Jädersten (M)

Center for Hematology and Regenerative Medicine, Department of Medicine Huddinge, Karolinska Institutet, Stockholm, Sweden.
Department of Hematology, Karolinska University Hospital, Stockholm, Sweden.

Selma Olsson Åkefeldt (SO)

Childhood Cancer Research Unit, Department of Women's and Children's Health, Karolinska Institutet, Stockholm, Sweden.
Department of Pediatric Infectious Diseases, Karolinska University Hospital, Stockholm, Sweden.

Mattias Svensson (M)

Center for Infectious Medicine, Department of Medicine Huddinge, Karolinska Institutet, Stockholm, Sweden.

George Kannourakis (G)

Fiona Elsey Cancer Research Institute and Federation University Australia, Ballarat, Vic., Australia.

Yenan T Bryceson (YT)

Center for Hematology and Regenerative Medicine, Department of Medicine Huddinge, Karolinska Institutet, Stockholm, Sweden.

Julien Haroche (J)

Institut E3M, Centre National de Référence des Histiocytoses, Hôpital Pitié-Salpêtrière, Sorbonne Université, Paris, France.

Jan-Inge Henter (JI)

Childhood Cancer Research Unit, Department of Women's and Children's Health, Karolinska Institutet, Stockholm, Sweden.
Department of Pediatric Oncology, Karolinska University Hospital, Stockholm, Sweden.

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