Omovertebral bone causing traumatic compression of the cervical spinal cord and acute neurological deficits in a patient with Sprengel's deformity and Klippel-Feil syndrome: case report.

Klippel-Feil syndrome Sprengel’s deformity acute neurological deficits congenital omovertebral bone traumatic spinal cord compression

Journal

Journal of neurosurgery. Spine
ISSN: 1547-5646
Titre abrégé: J Neurosurg Spine
Pays: United States
ID NLM: 101223545

Informations de publication

Date de publication:
25 Sep 2020
Historique:
received: 03 03 2020
accepted: 04 06 2020
medline: 26 9 2020
pubmed: 26 9 2020
entrez: 25 9 2020
Statut: epublish

Résumé

The presence of an omovertebral bone with Sprengel's deformity and Klippel-Feil syndrome is a complex congenital anomaly that is not well understood. It most commonly manifests as cosmetic deformity, limited range of motion, and functional disability, although there are reports of the insidious development of cervical myelopathy. In this paper, the authors present the case of a 49-year-old man with acute neurological deficits after a low-energy mechanism of traumatic spinal cord compression, resulting from an impinging omovertebral bone through a traumatic laminar defect. The patient underwent resection of the omovertebral bone, laminectomy decompression of the spinal canal, and anterior stabilization. This case highlights a rarely discussed complication of undiagnosed Sprengel's deformity and its associated conditions following even low-energy traumatic mechanisms.

Identifiants

pubmed: 32977313
doi: 10.3171/2020.6.SPINE20304
pii: 2020.6.SPINE20304
doi:

Types de publication

Case Reports

Langues

eng

Sous-ensembles de citation

IM

Pagination

32-36

Auteurs

Michael Pompliano (M)

1Department of Orthopedic Surgery, St. Joseph's University Medical Center, Paterson; and.

Stuart Changoor (S)

1Department of Orthopedic Surgery, St. Joseph's University Medical Center, Paterson; and.

Samuel Mease (S)

1Department of Orthopedic Surgery, St. Joseph's University Medical Center, Paterson; and.

Cyrus Emami (C)

2University Spine Center, Wayne, New Jersey.

Kumar Sinha (K)

1Department of Orthopedic Surgery, St. Joseph's University Medical Center, Paterson; and.
2University Spine Center, Wayne, New Jersey.

Ki Soo Hwang (KS)

1Department of Orthopedic Surgery, St. Joseph's University Medical Center, Paterson; and.
2University Spine Center, Wayne, New Jersey.

Classifications MeSH