Omovertebral bone causing traumatic compression of the cervical spinal cord and acute neurological deficits in a patient with Sprengel's deformity and Klippel-Feil syndrome: case report.
Klippel-Feil syndrome
Sprengel’s deformity
acute neurological deficits
congenital
omovertebral bone
traumatic spinal cord compression
Journal
Journal of neurosurgery. Spine
ISSN: 1547-5646
Titre abrégé: J Neurosurg Spine
Pays: United States
ID NLM: 101223545
Informations de publication
Date de publication:
25 Sep 2020
25 Sep 2020
Historique:
received:
03
03
2020
accepted:
04
06
2020
medline:
26
9
2020
pubmed:
26
9
2020
entrez:
25
9
2020
Statut:
epublish
Résumé
The presence of an omovertebral bone with Sprengel's deformity and Klippel-Feil syndrome is a complex congenital anomaly that is not well understood. It most commonly manifests as cosmetic deformity, limited range of motion, and functional disability, although there are reports of the insidious development of cervical myelopathy. In this paper, the authors present the case of a 49-year-old man with acute neurological deficits after a low-energy mechanism of traumatic spinal cord compression, resulting from an impinging omovertebral bone through a traumatic laminar defect. The patient underwent resection of the omovertebral bone, laminectomy decompression of the spinal canal, and anterior stabilization. This case highlights a rarely discussed complication of undiagnosed Sprengel's deformity and its associated conditions following even low-energy traumatic mechanisms.
Identifiants
pubmed: 32977313
doi: 10.3171/2020.6.SPINE20304
pii: 2020.6.SPINE20304
doi:
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM