Hemoglobinopathy E in 4 siblings of a North Indian family: A hidden malaise of social problem.

Chromosomal translocation hemoglobin E induced abortion sex ratio

Journal

Journal of family medicine and primary care
ISSN: 2249-4863
Titre abrégé: J Family Med Prim Care
Pays: India
ID NLM: 101610082

Informations de publication

Date de publication:
Jun 2020
Historique:
received: 21 01 2020
revised: 13 03 2020
accepted: 03 04 2020
entrez: 28 9 2020
pubmed: 29 9 2020
medline: 29 9 2020
Statut: epublish

Résumé

The preference for male child and neglect of girl child for long has resulted in a hazardously poor sex ratio, but bride buying seems to be no solution for it as it has its own inherent consequences on society and public health. This article tries to look at a relationship between a state's poorly kept secret like bride buying and its unseen complications. Here, we report a family of six members, where all 4 children have hemoglobin E disease a relatively rare entity seen in this part of the country. Hemoglobin E (β26 Glu → Lys) is usually seen in northeastern parts of India. This case report has tried to highlight a relatively rare disease afflicting all children of the family due to gene mutations which are rarely seen in Haryana/Punjab.

Identifiants

pubmed: 32984192
doi: 10.4103/jfmpc.jfmpc_135_20
pii: JFMPC-9-3160
pmc: PMC7491792
doi:

Types de publication

Case Reports

Langues

eng

Pagination

3160-3161

Informations de copyright

Copyright: © 2020 Journal of Family Medicine and Primary Care.

Déclaration de conflit d'intérêts

There are no conflicts of interest.

Références

Indian J Pathol Microbiol. 2009 Jan-Mar;52(1):110-2
pubmed: 19136801
PLoS One. 2019 Nov 21;14(11):e0225457
pubmed: 31751397
Orphanet J Rare Dis. 2020 Jan 15;15(1):15
pubmed: 31941534
Blood. 1996 Feb 1;87(3):887-92
pubmed: 8562958

Auteurs

Kapil Bhalla (K)

Department of Paediatrics, Pt BD Sharma PGIMS, Rohtak, Haryana, India.

Jatin Mangla (J)

Department of Paediatrics, Pt BD Sharma PGIMS, Rohtak, Haryana, India.

Ashish Gupta (A)

Department of Cardiology, Pt BD Sharma PGIMS, Rohtak, Haryana, India.

Sanjiv Nanda (S)

Department of Paediatrics, Pt BD Sharma PGIMS, Rohtak, Haryana, India.

Deepak Nehra (D)

Department of Pharmacology, Pt BD Sharma PGIMS, Rohtak, Haryana, India.

Classifications MeSH