Livedo Racemosa - The Pathophysiology of Decompression-Associated Cutis Marmorata and Right/Left Shunt.

PFO cutis marmorata decompression illness livedo racemosa livedo reticularis patent ovale foramen right/left shunt skin bends

Journal

Frontiers in physiology
ISSN: 1664-042X
Titre abrégé: Front Physiol
Pays: Switzerland
ID NLM: 101549006

Informations de publication

Date de publication:
2020
Historique:
received: 21 04 2020
accepted: 22 07 2020
entrez: 5 10 2020
pubmed: 6 10 2020
medline: 6 10 2020
Statut: epublish

Résumé

Decompression sickness and arterial gas embolism, collectively known as decompression illness (DCI), are serious medical conditions that can result from compressed gas diving. DCI can present with a wide range of physiologic and neurologic symptoms. In diving medicine, skin manifestations are usually described in general as cutis marmorata (CM). Mainly in the Anglo-American literature the terms cutis marmorata, livedo reticularis (LR), and livedo racemosa (LRC) are used interchangeably but actually describe pathophysiologically different phenomena. CM is a synonym for LR, which is a physiological and benign, livid circular discoloration with a net-like, symmetric, reversible, and uniform pattern. The decompression-associated skin discolorations, however, correspond to the pathological, irregular, broken netlike pattern of LRC. Unlike in diving medicine, in clinical medicine/dermatology the pathology of livedo racemosa is well described as a thrombotic/embolic occlusion of arteries. This concept of arterial occlusion suggests that the decompression-associated livedo racemosa may be also caused by arterial gas embolism. Recent studies have shown a high correlation of cardiac right/left (R/L) shunts with arterial gas embolism and skin bends in divers with unexplained DCI. To further investigate this hypothesis, a retrospective analysis was undertaken in a population of Austrian, Swiss, and German divers. The R/L shunt screening results of 18 divers who suffered from an unexplained decompression illness (DCI) and presented with livedo racemosa were retrospectively analyzed. All of the divers were diagnosed with a R/L shunt, 83% with a cardiac shunt [patent foramen ovale (PFO)/atrium septum defect (ASD)], and 17% with a non-cardiac shunt. We therefore not only confirm this hypothesis but when using appropriate echocardiographic techniques even found a 100% match between skin lesions and R/L shunt. In conclusion, in diving medicine the term cutis marmorata/livedo reticularis is used incorrectly for describing the actual pathology of livedo racemosa. Moreover, this pathology could be a good explanation for the high correlation of livedo racemosa with cardiac and non-cardiac right/left shunts in divers without omission of decompression procedures.

Identifiants

pubmed: 33013436
doi: 10.3389/fphys.2020.00994
pmc: PMC7497564
doi:

Types de publication

Journal Article

Langues

eng

Pagination

994

Informations de copyright

Copyright © 2020 Hartig, Reider, Sojer, Hammer, Ploner, Muth, Tilg and Köhler.

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Auteurs

Frank Hartig (F)

Department of Internal Medicine, University Clinic Innsbruck, Innsbruck, Austria.

Norbert Reider (N)

Department of Dermatology, University Clinic Innsbruck, Innsbruck, Austria.

Martin Sojer (M)

Department of Neurology, University Clinic Innsbruck, Innsbruck, Austria.

Alexander Hammer (A)

Department of Internal Medicine, University Clinic Innsbruck, Innsbruck, Austria.

Thomas Ploner (T)

Department of Internal Medicine, University Clinic Innsbruck, Innsbruck, Austria.

Claus-Martin Muth (CM)

Department of Anaesthesiology, University Clinic Ulm, Ulm, Germany.

Herbert Tilg (H)

Department of Internal Medicine, University Clinic Innsbruck, Innsbruck, Austria.

Andrea Köhler (A)

Department of Internal Medicine, University Clinic Innsbruck, Innsbruck, Austria.

Classifications MeSH