Hematopoietic Stem Cell Transplantation and Vasculopathy Associated With STAT3-Dominant-Negative Hyper-IgE Syndrome.

Job's syndrome ST elevation myocardial infarction STAT3 transcription factor cardiovascular diseases coronary vessels counseling hematopoietic stem cell transplantation thrombosis

Journal

Frontiers in pediatrics
ISSN: 2296-2360
Titre abrégé: Front Pediatr
Pays: Switzerland
ID NLM: 101615492

Informations de publication

Date de publication:
2020
Historique:
received: 10 06 2020
accepted: 06 08 2020
entrez: 5 10 2020
pubmed: 6 10 2020
medline: 6 10 2020
Statut: epublish

Résumé

Dominant negative mutations in the transcription-factor

Identifiants

pubmed: 33014947
doi: 10.3389/fped.2020.00575
pmc: PMC7511721
doi:

Types de publication

Case Reports

Langues

eng

Pagination

575

Informations de copyright

Copyright © 2020 Ponsford, Clark, Mock, Abinun, Carne, El-Shanawany, Williams, Choudhury, Freeman, Gennery and Jolles.

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Auteurs

Mark J Ponsford (MJ)

Immunodeficiency Centre for Wales, University Hospital for Wales, Cardiff, United Kingdom.
Division of Infection, Inflammation, and Immunity, School of Medicine, Tenovus Institute, Cardiff University, Cardiff, United Kingdom.

James Clark (J)

Department of Interventional Cardiology, University Hospital for Wales, Cardiff, United Kingdom.

Joel Mock (J)

Department of Interventional Cardiology, University Hospital for Wales, Cardiff, United Kingdom.

Mario Abinun (M)

Paediatric Haematopoietic Stem Cell Transplant Unit, Translational and Clinical Research Institute, Great North Children's Hospital, Newcastle University, Newcastle upon Tyne, United Kingdom.

Emily Carne (E)

Immunodeficiency Centre for Wales, University Hospital for Wales, Cardiff, United Kingdom.

Tariq El-Shanawany (T)

Immunodeficiency Centre for Wales, University Hospital for Wales, Cardiff, United Kingdom.

Paul E Williams (PE)

Immunodeficiency Centre for Wales, University Hospital for Wales, Cardiff, United Kingdom.

Anirban Choudhury (A)

Department of Interventional Cardiology, Morriston Hospital, Swansea Bay University Local Health Board, Swansea, United Kingdom.

Alexandra F Freeman (AF)

Laboratory of Clinical Immunology and Microbiology, National Institute of Allergy and Infectious Diseases, National Institutes of Health, Bethesda, MD, United States.

Andrew R Gennery (AR)

Paediatric Haematopoietic Stem Cell Transplant Unit, Translational and Clinical Research Institute, Great North Children's Hospital, Newcastle University, Newcastle upon Tyne, United Kingdom.

Stephen Jolles (S)

Immunodeficiency Centre for Wales, University Hospital for Wales, Cardiff, United Kingdom.

Classifications MeSH