Jervell and Lange-Nielsen syndrome with novel KCNQ1 and additional gene mutations.

Disease genetics Genetic counselling

Journal

Human genome variation
ISSN: 2054-345X
Titre abrégé: Hum Genome Var
Pays: England
ID NLM: 101652445

Informations de publication

Date de publication:
2020
Historique:
received: 08 12 2019
revised: 19 08 2020
accepted: 14 09 2020
entrez: 21 10 2020
pubmed: 22 10 2020
medline: 22 10 2020
Statut: epublish

Résumé

We encountered a boy with Jervell and Lange-Nielsen syndrome (JLNS) with compound heterozygous

Identifiants

pubmed: 33082985
doi: 10.1038/s41439-020-00121-x
pii: 121
pmc: PMC7562699
doi:

Types de publication

Journal Article

Langues

eng

Pagination

34

Informations de copyright

© The Author(s) 2020.

Déclaration de conflit d'intérêts

Conflict of interestThe authors declare that they have no conflict of interest.

Références

Circ J. 2008 May;72(5):687-93
pubmed: 18441444
Circ Arrhythm Electrophysiol. 2009 Dec;2(6):667-76
pubmed: 20009079
Circulation. 2000 Dec 5;102(23):2849-55
pubmed: 11104743
Circ Cardiovasc Genet. 2013 Aug;6(4):313-6
pubmed: 23963159
Circulation. 2006 Feb 14;113(6):783-90
pubmed: 16461811
Cardiology. 2016;133(2):73-8
pubmed: 26496715
Hum Genet. 2000 Nov;107(5):499-503
pubmed: 11140949
Circulation. 1995 Nov 15;92(10):2929-34
pubmed: 7586261
Ann Med. 2004;36 Suppl 1:53-63
pubmed: 15176425
Circulation. 1993 Jun;87(6):1866-72
pubmed: 8099317
Am Heart J. 1957 Jul;54(1):59-68
pubmed: 13435203
ISRN Cardiol. 2012;2012:846171
pubmed: 23304551
N Engl J Med. 1992 Sep 17;327(12):846-52
pubmed: 1508244
Genet Med. 2015 May;17(5):405-24
pubmed: 25741868
N Engl J Med. 2003 May 8;348(19):1866-74
pubmed: 12736279
Circulation. 2004 Apr 20;109(15):1834-41
pubmed: 15051636
J Biol Chem. 1999 Jul 23;274(30):21063-70
pubmed: 10409658

Auteurs

Shinichi Matsuda (S)

Department of Pediatrics, Tokai University School of Medicine, Isehara, Japan.

Yuko Ohnuki (Y)

Department of Medical Ethics, Tokai University School of Medicine, Isehara, Japan.
Department of Clinical Genetics, Tokai University Hospital, Isehara, Japan.

Mayuri Okami (M)

Department of Clinical Genetics, Tokai University Hospital, Isehara, Japan.
Department of Otolaryngology, Tokai University School of Medicine, Isehara, Japan.
Department of Otolaryngology, Samukawa Hospital, Samukawa, Japan.

Eriko Ochiai (E)

Department of Forensic Medicine, Tokai University School of Medicine, Isehara, Japan.

Shiro Yamada (S)

Department of Pediatrics, Tokai University Oiso Hospital, Oiso, Japan.

Kazumi Takahashi (K)

Department of Medical Ethics, Tokai University School of Medicine, Isehara, Japan.
Department of Clinical Genetics, Tokai University Hospital, Isehara, Japan.

Motoki Osawa (M)

Department of Forensic Medicine, Tokai University School of Medicine, Isehara, Japan.

Kenji Okami (K)

Department of Otolaryngology, Tokai University School of Medicine, Isehara, Japan.

Masahiro Iida (M)

Department of Otolaryngology, Tokai University School of Medicine, Isehara, Japan.

Hiroyuki Mochizuki (H)

Department of Pediatrics, Tokai University School of Medicine, Isehara, Japan.

Classifications MeSH