A longitudinal and transancestral analysis of DNA methylation patterns and disease activity in lupus patients.


Journal

JCI insight
ISSN: 2379-3708
Titre abrégé: JCI Insight
Pays: United States
ID NLM: 101676073

Informations de publication

Date de publication:
19 11 2020
Historique:
received: 25 08 2020
accepted: 14 10 2020
pubmed: 28 10 2020
medline: 8 6 2021
entrez: 27 10 2020
Statut: epublish

Résumé

Epigenetic dysregulation is implicated in the pathogenesis of lupus. We performed a longitudinal analysis to assess changes in DNA methylation in lupus neutrophils over 4 years of follow-up and across disease activity levels using 229 patient samples. We demonstrate that DNA methylation profiles in lupus are partly determined by ancestry-associated genetic variations and are highly stable over time. DNA methylation levels in 2 CpG sites correlated significantly with changes in lupus disease activity. Progressive demethylation in SNX18 was observed with increasing disease activity in African American patients. Importantly, demethylation of a CpG site located within GALNT18 was associated with the development of active lupus nephritis. Differentially methylated genes between African American and European American lupus patients include type I IFN-response genes such as IRF7 and IFI44, and genes related to the NF-κB pathway. TREML4, which plays a vital role in TLR signaling, was hypomethylated in African American patients and demonstrated a strong cis-methylation quantitative trait loci (cis-meQTL) effect among 8855 cis-meQTL associations identified in our study.

Identifiants

pubmed: 33108347
pii: 143654
doi: 10.1172/jci.insight.143654
pmc: PMC7710270
doi:
pii:

Substances chimiques

Biomarkers 0
IRF7 protein, human 0
Interferon Regulatory Factor-7 0
Receptors, Immunologic 0
SNX18 protein, human 0
Sorting Nexins 0
TREML4 protein, human 0

Types de publication

Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : NIAID NIH HHS
ID : R01 AI097134
Pays : United States
Organisme : NIAID NIH HHS
ID : U19 AI110502
Pays : United States

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Auteurs

Patrick Coit (P)

Division of Rheumatology, Department of Pediatrics, University of Pittsburgh, Pittsburgh, Pennsylvania, USA.
Graduate Program in Immunology and.

Lourdes Ortiz-Fernandez (L)

Division of Rheumatology, Department of Pediatrics, University of Pittsburgh, Pittsburgh, Pennsylvania, USA.

Emily E Lewis (EE)

Division of Rheumatology, Department of Internal Medicine, University of Michigan, Ann Arbor, Michigan, USA.

W Joseph McCune (WJ)

Division of Rheumatology, Department of Internal Medicine, University of Michigan, Ann Arbor, Michigan, USA.

Kathleen Maksimowicz-McKinnon (K)

Division of Rheumatology, Henry Ford Health System, Detroit, Michigan, USA.

Amr H Sawalha (AH)

Division of Rheumatology, Department of Pediatrics, University of Pittsburgh, Pittsburgh, Pennsylvania, USA.
Division of Rheumatology and Clinical Immunology, Department of Medicine, University of Pittsburgh, Pennsylvania, USA.
Lupus Center of Excellence, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania, USA.
Department of Immunology, University of Pittsburgh, Pittsburgh, Pennsylvania, USA.

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