Deciphering the Genetics of Primary Angioedema with Normal Levels of C1 Inhibitor.

next-generation sequencing pedigree analysis primary angioedema primary angioedema with normal C1 inhibitor

Journal

Journal of clinical medicine
ISSN: 2077-0383
Titre abrégé: J Clin Med
Pays: Switzerland
ID NLM: 101606588

Informations de publication

Date de publication:
23 Oct 2020
Historique:
received: 23 09 2020
revised: 13 10 2020
accepted: 19 10 2020
entrez: 29 10 2020
pubmed: 30 10 2020
medline: 30 10 2020
Statut: epublish

Résumé

The genetic alteration underlying the great majority of primary angioedema with normal C1 inhibitor (nl-C1-INH-HAE) cases remains unknown. To search for variants associated with nl-C1-INH-HAE, we genotyped 133 unrelated nl-C1-INH-HAE patients using a custom next-generation sequencing platform targeting 55 genes possibly involved in angioedema pathogenesis. Patients already diagnosed with

Identifiants

pubmed: 33114181
pii: jcm9113402
doi: 10.3390/jcm9113402
pmc: PMC7690775
pii:
doi:

Types de publication

Journal Article

Langues

eng

Subventions

Organisme : Shire International GmbH, a member of the Takeda group of companies
ID : IIR-GRC-000905

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Auteurs

Gedeon Loules (G)

CeMIA SA, Makriyianni 31, GR-41334 Larissa, Greece.

Faidra Parsopoulou (F)

CeMIA SA, Makriyianni 31, GR-41334 Larissa, Greece.
Department of Immunology & Histocompatibility, School of Health Sciences, Faculty of Medicine, University of Thessaly, Panepistimiou 3, GR-41500 Biopolis, Larissa, Greece.

Maria Zamanakou (M)

CeMIA SA, Makriyianni 31, GR-41334 Larissa, Greece.

Dorottya Csuka (D)

Hungarian Angioedema Center, 3rd Department of Internal Medicine, Semmelweis University, Kutvolgyi ut 4, H-1125 Budapest, Hungary.

Maria Bova (M)

Department of Translational Medicine, University of Naples, Via S. Pansini 5, 80131 Naples, Italy.

Teresa González-Quevedo (T)

Reference Unit for Angioedema in Andalusia, Allergy Department, Virgen del Rocío University Hospital, Av Manuel Siurot s/n, 41013 Seville, Spain.

Fotis Psarros (F)

Department of Allergology, Navy Hospital, Deinokratous 70, GR-11521 Athens, Greece.

Gregor Porebski (G)

Department of Clinical and Environmental Allergology, Jagiellonian University Medical College, Sniadeckich 10, 31-531 Krakow, Poland.

Matthaios Speletas (M)

Department of Immunology & Histocompatibility, School of Health Sciences, Faculty of Medicine, University of Thessaly, Panepistimiou 3, GR-41500 Biopolis, Larissa, Greece.

Davide Firinu (D)

Department of Medical Sciences and Public Health, University of Cagliari, 09042 Monserrato, Italy.

Stefano Del Giacco (S)

Department of Medical Sciences and Public Health, University of Cagliari, 09042 Monserrato, Italy.

Chiara Suffritti (C)

Department of Biomedical and Clinical Sciences Luigi Sacco, University of Milan, Via G.B. Grassi 74, 20157 Milan, Italy.

Michael Makris (M)

Allergy Unit, 2nd Department of Dermatology and Venereology, National and Kapodistrian University of Athens, University Hospital "Attikon", Rimini 1, GR-12462 Chaidari, Athens, Greece.

Sofia Vatsiou (S)

CeMIA SA, Makriyianni 31, GR-41334 Larissa, Greece.
Department of Immunology & Histocompatibility, School of Health Sciences, Faculty of Medicine, University of Thessaly, Panepistimiou 3, GR-41500 Biopolis, Larissa, Greece.

Andrea Zanichelli (A)

Department of Biomedical and Clinical Sciences Luigi Sacco, University of Milan, Via G.B. Grassi 74, 20157 Milan, Italy.

Henriette Farkas (H)

Hungarian Angioedema Center, 3rd Department of Internal Medicine, Semmelweis University, Kutvolgyi ut 4, H-1125 Budapest, Hungary.

Anastasios E Germenis (AE)

CeMIA SA, Makriyianni 31, GR-41334 Larissa, Greece.
Department of Immunology & Histocompatibility, School of Health Sciences, Faculty of Medicine, University of Thessaly, Panepistimiou 3, GR-41500 Biopolis, Larissa, Greece.

Classifications MeSH