Tuberculosis-associated HLH in a patient with chronic kidney disease on haemodialysis.


Journal

Oxford medical case reports
ISSN: 2053-8855
Titre abrégé: Oxf Med Case Reports
Pays: England
ID NLM: 101642070

Informations de publication

Date de publication:
Oct 2020
Historique:
received: 07 05 2020
revised: 16 06 2020
accepted: 30 07 2020
entrez: 2 11 2020
pubmed: 3 11 2020
medline: 3 11 2020
Statut: epublish

Résumé

Haemophagocytic lymphohistiocytosis (HLH) is a rare immunological disorder that is accompanied by a high mortality rate when the underlying aetiology is miliary tuberculosis. We report a case of tuberculosis (TB)-associated HLH in a haemodialysis patient, from a TB-endemic region, who missed two sessions of dialysis before developing the primary symptoms of HLH. The patient presented with non-specific findings including pancytopenia, coagulopathy and transaminitis. Computer-tomography imaging and microbiology from bronchoalveolar lavage evidenced miliary tuberculosis. Further testing revealed the TB-associated-HLH characteristic pattern of thrombocytosis, leukopenia, transaminitis, hyperferritinemia and elevated fibrinogen. The patient initially demonstrated improvement after initiation of anti-TB therapy. However, soon thereafter began to paradoxically deteriorate and then expire from apparent tuberculosis-immune reconstitution inflammatory syndrome. This case highlights the importance of early diagnosis and treatment, and consequently of the utility of diagnostic systems such as the HScore in cases of high clinical suspicion.

Identifiants

pubmed: 33133616
doi: 10.1093/omcr/omaa082
pii: omaa082
pmc: PMC7583401
doi:

Types de publication

Case Reports

Langues

eng

Pagination

omaa082

Informations de copyright

© The Author(s) 2020. Published by Oxford University Press. All rights reserved. For Permissions, please email: journals.permissions@oup.com.

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Auteurs

Pouria Shoureshi (P)

Department of Internal Medicine, Orange Park Medical Center, Orange Park, FL, USA.

Johanna Ruiz (J)

Department of Internal Medicine, Orange Park Medical Center, Orange Park, FL, USA.

Ahmad Abdulzahir (A)

Department of Internal Medicine, Orange Park Medical Center, Orange Park, FL, USA.

Alexander L Bisch (AL)

Medical student, Department of Internal Medicine, Edward Via College of Osteopathic Medicine- Carolinas, Spartanburg, SC, USA.

Naja Naddaf (N)

Core faculty, Department of Internal Medicine, Orange Park Medical Center, Orange Park, FL, USA.

Justin Gisel (J)

Core faculty, Department of Internal Medicine, Orange Park Medical Center, Orange Park, FL, USA.

Classifications MeSH